Results 11 to 20 of about 2,851 (167)

An Exceedingly Rare Case of Mechanobullous Epidermolysis Bullosa Acquisita in a Prepubertal Child: A Review of the Clinical and Laboratory Considerations [PDF]

Antibodies
Introduction: Epidermolysis bullosa acquisita (EBA) is a rare autoimmune disease causing subepithelial blistering due to autoantibodies against type VII collagen.
Aleksandra Wiktoria Bratborska, Maciej Spałek, Monika Bowszyc-Dmochowska, Marian Dmochowski   +3 more
doaj   +2 more sources

Complexities of care in a pediatric patient with epidermolysis bullosa acquisita and duchenne muscular dystrophy: a case report [PDF]

Journal of Medical Case Reports
Background Type VII collagen autoantibodies drive epidermolysis bullosa acquisita (EBA), a rare autoimmune blistering disorder. While typically seen in adults, pediatric cases—especially those with additional comorbidities—present unique clinical ...
Khayry Al-Shami, Ziad Haddad, Malath Mohammad Yousef Abuelrub, Basel Adnan Adel Qaddoumi, Falah Qudah, Tala Abdelaziz Abdullateef Shandaq, Manar Al-Shami, Saja Karaja   +7 more
doaj   +2 more sources

Diagnosis of Epidermolysis Bullosa Acquisita: Multicentre Comparison of Different Assays for Serum Anti-type VII Collagen Reactivity [PDF]

Acta Dermato-Venereologica, 2021
Epidermolysis bullosa acquisita is a pemphigoid disease characterized by autoantibodies against type VII collagen. This study compared the sensitivity and specificity of 6 diagnostic assays: type VII collagen non-collagenous domains enzyme-linked ...
Maike M. Holtsche, Nina van Beek, Takashi Hashimoto, Giovanni Di Zenzo, Detlef Zillikens, Catherine Prost-Squarcioni, Matthias Titeux, Alain Hovnanian, Enno Schmidt, Stephanie Goletz   +9 more
doaj   +2 more sources

Clinical Features of Paediatric Inflammatory Epidermolysis Bullosa Acquisita: A Case Series Study [PDF]

Acta Dermato-Venereologica
Epidermolysis bullosa acquisita (EBA) rarely develops in childhood. This study retrospectively recruited paediatric patients with EBA (age ≤ 16 years), diagnosed by clinical and histopathological features and results of immunofluorescence, immunoblotting
Yuexin Zhang, Jingyang Dang, Ruoyu Li, Xixue Chen, Xuejun Zhu, Mingyue Wang   +5 more
doaj   +2 more sources

Inhibition of interferon gamma impairs induction of experimental epidermolysis bullosa acquisita [PDF]

Frontiers in Immunology
Epidermolysis bullosa acquisita (EBA) is a muco-cutaneous autoimmune disease characterized and caused by autoantibodies targeting type VII collagen (COL7). The treatment of EBA is notoriously difficult, with a median time to remission of 9 months.
Natalie Gross, Jana Marketon, Sadegh Mousavi, Kathrin Kalies, Ralf J. Ludwig, Ralf J. Ludwig, Katja Bieber   +6 more
doaj   +2 more sources

Epidermolysis Bullosa Acquisita

Indian Journal of Dermatology, 1997
A 35 years old man presented with features of epidermolysis bullosa acquisita. Here is the case report.
Gangopadhyay Asok Kumar
doaj   +3 more sources

IgM-mediated epidermolysis bullosa acquisita [PDF]

JAAD Case Reports
Sidney Harrison, BS, Vita Mayes, PA-C, MSc, MPH, MMSc, Conrad Brimhall, MD, Roy King, MD   +3 more
doaj   +2 more sources

Epidermolysis bullosa acquisita: A report of four cases

Indian Journal of Dermatology, 2022
Abhishek De, Subhra Dhar, Raghavendra Rao, Aarti Sarda, Sandipan Dhar   +4 more
doaj   +2 more sources

Whole-genome expression Profiling in skin reveals sYK as a Key regulator of inflammation in experimental epidermolysis Bullosa acquisita [PDF]

, 2018
Because of the morbidity and limited therapeutic options of autoimmune diseases, there is a high, and thus far, unmet medical need for development of novel treatments.
Aga, Behnen, Bieber, Bieber, Buijsrogge, Carvalho, Chen, Chiriac, Corr, Dorward, Efron, Futosi, Geahlen, Genovese, Hellberg, Hirose, Hirose, Huang, Iwata, Jakus, Kalies, Karsten, Kasperkiewicz, Kasperkiewicz, Kasprick, Kasprick, Kemmer, Kleinau, Koga, Kovács, Kulkarni, Langfelder, Langfelder, Lin, Ludwig, Ludwig, Ludwig, Mihai, Mocsai, Müller, Németh, Németh, Patterson, Pihur, Pliyev, Recke, Recke, Renckens, Sadeghi, Sadeghi, Schmidt, Sezin, Shimanovich, Sitaru, van der Steen, Xue, Yamamoto, Zhao   +57 more
core   +10 more sources

Diagnostic Value and Practicability of Serration Pattern Analysis by Direct Immunofluorescence Microscopy in Pemphigoid Diseases

Acta Dermato-Venereologica, 2021
In pemphigoid diseases, direct immunofluorescence can be used to differentiate 2 patterns of antibody deposition at the dermal–epidermal junction; u- and n-serrated pattern.
Maike M. Holtsche, Nina van Beek, Axel Künstner, Hauke Busch, Detlef Zillikens, Enno Schmidt   +5 more
doaj   +1 more source