Results 11 to 20 of about 99,710 (159)

Atypical Anti-Glomerular Basement Membrane Disease

Kidney International Reports, 2023
Atypical anti-glomerular basement membrane (anti-GBM) disease is characterized by linear immunoglobulin G (IgG) deposition along the GBM without circulating IgG anti-GBM antibodies. Compared to classic anti-GBM disease, atypical anti-GBM disease tends to
Joyita Bharati, Yi-He Yang, Purva D. Sharma, K. Jhaveri   +3 more
semanticscholar   +1 more source

Anti-Glomerular Basement Membrane Disease in a 10-year-old Child: A Case Report

Journal of Nepal Medical Association, 2023
Anti-glomerular basement membrane disease is an extremely uncommon entity in children. It has an incidence of 0.5 to 1 per million per year in adults and is even more uncommon in children.
Md Firoz Anjum, Sajal Twanabasu, Sailesh Shrestha, Tashi Anjuk Lama, Dipendra Magrati   +4 more
doaj   +1 more source

Anti-GBM disease with positive serum anti-GBM antibodies but negative IgG deposition: A case report

SAGE Open Medical Case Reports, 2023
Anti-glomerular basement membrane antibodies are significantly specific for detecting anti-glomerular basement membrane disease. These antibodies are typically targeted against the non-collagenous (NC1) domain of the alpha 3 chain of type IV collagen and,
Kimia Kazemzadeh, Elham Kabiri Naeini, Firouzeh Moeinzadeh, Azar Naimi   +3 more
doaj   +1 more source

Molecular and Cellular Mechanisms Underlying the Initiation and Progression of Alport Glomerular Pathology

Frontiers in Medicine, 2022
Alport syndrome results from a myriad of variants in the COL4A3, COL4A4, or COL4A5 genes that encode type IV (basement membrane) collagens. Unlike type IV collagen α1(IV)2α2(IV)1 heterotrimers, which are ubiquitous in basement membranes, α3/α4/α5 have a ...
Dominic Cosgrove, Jacob Madison
doaj   +1 more source

Anti-Glomerular Basement Membrane Disease

Definitions, 2020
Anti-glomerular basement membrane disease (anti-GBM) is a rare but well-characterized cause of glomerulonephritis. It is defined by the presence of autoantibodies directed at specific antigenic targets within the glomerular and/or pulmonary basement ...
A. Rees
semanticscholar   +1 more source

Tubular basement membrane deposits after allogeneic hematopoietic stem cell transplantation

BMC Nephrology, 2023
Background Extraglomerular immune complex deposition is rare and only a few membranous nephropathy cases with tubular basement membrane deposits have been reported following allogeneic hematopoietic stem cell transplantation.
Wenyan Zhou, Chaojun Qi, Minfang Zhang, Xiaotao Hou, Zhaohui Ni   +4 more
doaj   +1 more source

Etanercept-Induced Anti-Glomerular Basement Membrane Disease

Case Reports in Nephrology and Dialysis, 2021
Anti-glomerular basement membrane (anti-GBM) disease is a rare form of small-vessel vasculitis that typically causes rapidly progressive glomerulonephritis with or without alveolar haemorrhage.
Saif Al-Chalabi, Henry H.L. Wu, Rajkumar Chinnadurai, Arvind Ponnusamy   +3 more
doaj   +1 more source

Prevalence of clinical, pathological and molecular features of glomerular basement membrane nephropathy caused by COL4A3 or COL4A4 mutations: a systematic review

Clinical Kidney Journal, 2020
Background Patients heterozygous for COL4A3 or COL4A4 mutations show a wide spectrum of disease, extending from familial isolated microscopic haematuria, as a result of thin basement membranes (TBMs), to autosomal dominant Alport syndrome (ADAS) and end ...
Andreas M. Matthaiou, Tsielestina Poulli, C. Deltas   +2 more
semanticscholar   +1 more source

Case Report of a Patient with Goodpasture’s Syndrome Who Relapsed While on Hemodialysis

Turkish Journal of Nephrology, 2019
Goodpasture’s syndrome is a rare autoimmune disease in which anti-glomerular basement membrane antibodies damage the glomerular and alveolar basement membrane. Its relapse is very rare, compared to other pulmonary-renal syndromes.
Tuba Elif ŞENEL, Sami UZUN, Egemen CEBECİ, Oktay ÖZKAN, Ahmet BEHLÜL, Ayça EROĞLU, Yasemin ÖZLÜK, Savaş ÖZTÜRK   +7 more
doaj   +1 more source

Anti-glomerular basement membrane disease superimposed on membranous nephropathy: a case report and review of the literature

Journal of Medical Case Reports, 2010
Introduction Anti-glomerular basement membrane disease is a rare autoimmune disorder characterized by pulmonary hemorrhage, crescentic glomerulonephritis and the presence of circulating anti-glomerular basement membrane antibodies.
Nivera Noel, Patel Dhruval, Tunkel Allan R   +2 more
doaj   +1 more source