Results 51 to 60 of about 1,722 (164)

Positive Clinical, Neuropsychological, and Metabolic Impact of Liver Transplantation in Patients With Argininosuccinate Lyase Deficiency

Journal of Inherited Metabolic Disease, Volume 48, Issue 1, January 2025.
ABSTRACT Liver transplantation (LTx) is increasingly used in Urea Cycle Defects (UCDs) to prevent recurrent hyperammonemia and related neurological irreversible injury. Among UCDs, argininosuccinate lyase deficiency (ASLD) has a more complex phenotype than other UCDs, with long‐term neurocognitive deficits.
Barbara Siri, Benedetta Greco, Diego Martinelli, Sara Cairoli, Alessia Guarnera, Daniela Longo, Antonio Napolitano, Chiara Parrillo, Lucilla Ravà, Raffaele Simeoli, Gionata Spagnoletti, Roberta Taurisano, Silvio Veraldi, Andrea Pietrobattista, Marco Spada, Carlo Dionisi‐Vici   +15 more
wiley   +1 more source

Proton Magnetic Resonance Spectroscopy of the Developing Human Brain

Clinical Neuroimaging, Volume 2, Issue 1, 2025.
ABSTRACT Neurodevelopmental disorders are pervasive and pose a significant public health problem. Many of these disorders can have a lifelong impact on the quality of life and may affect an individual's ability to function independently. In numerous pediatric and fetal neurological disorders, biochemical alterations precede or mediate structural and ...
Firoozeh Shomal Zadeh, Qinqin Yang, Ali Gholipour, Camilo Jaimes   +3 more
wiley   +1 more source

Hepatic metabolism of guanidinoacetic acid on broilers

Revista Brasileira de Zootecnia
ABSTRACT The objective of this study was to evaluate the hepatic metabolism and performance of broilers fed reduced-energy diets (50 kcal/kg less), with or without guanidinoacetic acid (GAA). A total of 432-day-old male chicks of the Cobb 500 lineage were distributed in a completely randomized design with three treatments and eight replications.
Paulo Henrique Sousa da Paz, Heloisa Helena de Carvalho Mello, Fabyola Barros de Carvalho, José Henrique Stringhini, Emmanuel Arnhold, Michel Blézins de Arruda, Isobel Margaret Whiting, Vasil Radoslavov Pirgozliev, Marcos Barcellos Café   +8 more
openaire   +2 more sources

Creatine Ameliorates the Adverse Effects of High‐Fat Diet on Hepatic Lipid Metabolism via Activating Mfn2‐Mediated Mitochondrial Fusion in Juvenile Grass Carp

Aquaculture Nutrition, Volume 2025, Issue 1, 2025.
With the increasing prevalence of high‐fat diets (HFD) in aquaculture practices, the detrimental effects of HFD on farmed fish have garnered significant attention. Creatine has emerged as a promising green feed additive for aquaculture species; however, its potential role in mitigating the negative impacts of HFD remains poorly understood.
Nan-Jun Hu, Guang-Li Feng, Xiao-Hong Lai, Mo Peng, Yu-Feng Song, Shouqi Xie   +5 more
wiley   +1 more source

Lack of Epileptogenic Effects of the Creatine Precursor Guanidinoacetic Acid on Neuronal Cultures In Vitro

, 2022
The creatine precursor Guanidinoacetic Acid (GAA) accumulates in the genetic deficiency of the GuanidinoAcetate Methyl Transferase (GAMT) enzyme and it is believed to cause the seizures that often occur in this condition.
Enrico Adriano, Massobrio, Paolo, Balestrino, Maurizio, Mariateresa Tedesco, Adriano, Enrico, Maurizio Balestrino, Poggio, Fabio, Brofiga, Martina, Tedesco, Mariateresa, Fabio Poggio, Martina Brofiga, Paolo Massobrio   +11 more
core   +1 more source

Guanidinoacetic acid piglets

, 2016
In the search for improved animal performance, has been testing new substances and new products to be used as additives in feed. Creatine and their precursors are examples of such compounds used for improvement of animal productivity. The guanidinoacetic
Teixeira, Karla Andrade
core  

Effects of supplemental creatine and guanidinoacetic acid on spatial memory and the brain of weaned Yucatan miniature pigs

, 2020
The emergence of creatine as a potential cognitive enhancement supplement for humans prompted an investigation as to whether supplemental creatine could enhance spatial memory in young swine.
Raniru Randunu (8232534), Rebecca A. Ryan (8232531), Gerard M. Martin (8232537), Gerard M Martin, Janet A Brunton, Jason L. Robinson (8232528), Rebecca A Ryan, Laura E McBreairty, Robert F. Bertolo (8232543), Jason L Robinson, Raniru Randunu, Carolyn J Walsh, Carolyn J. Walsh (7023983), Janet A. Brunton (8232540), Robert F Bertolo, Laura E. McBreairty (7436972)   +15 more
core   +1 more source

Pulmonary hypertensive response of broiler chickens to arginine and guanidinoacetic acid under high-altitude hypoxia [PDF]

, 2018
This study assessed the preventive effects of arginine (ARG) and guanidinoacetic acid (GAA) on the incidence of pulmonary hypertension syndrome (PHS) in broiler chickens.
Behnam Ahmadipour, Fariborz Khajali, Ahmadipour, Behnam, Sharifi, Mohammadreza, Khajali, Fariborz, Mohammadreza Sharifi   +5 more
core   +1 more source

Reducing broiler breast myopathies through supplementation of guanidinoacetic acid in broiler diets

, 2023
SUMMARY: Performance and processing advantages have been noted in meat animal production when excess arginine is available in the diet. In addition, dietary inclusion of guanidinoacetic acid (GAA) has provided insight on sparing arginine for broiler ...
D.S. Nelson, Rochell, S. J., C.M. Owens, Maynard, C. J., Nelson, D. S., S.J. Rochell, C.J. Maynard, Owens, C. M.   +7 more
core   +1 more source

Effect of Guanidinoacetic Acid Supplementation on Growth Performance and Gut Morpholog yin Broiler Chickens [PDF]

, 2018
This study evaluates the effects of different levels of guanidinoacetic acid (GAA) supplement on growth performance and gut morphology in broilers (Ross 308 strain) raised at high altitude (2100 m).
Khajali F, Sharifi MR, Ahmadipour B
core   +1 more source