Results 11 to 20 of about 11,909 (199)

Diagnosis, management and the burden of symptoms of mastocytosis from the physician's perspective: A nationwide study. [PDF]

Br J Haematol
Summary Mastocytosis is categorized into cutaneous mastocytosis (CM), mast cell sarcoma and systemic mastocytosis (SM). Within SM, indolent SM (ISM) is the more frequent subtype. Adult patients with CM but without an extracutaneous biopsy are classified as having mastocytosis in the skin (MIS), a provisional diagnosis.
Rossignol J, Bouillet L, Bulai-Livideanu C, Barete S, Bruneau J, Gourguechon C, Polivka L, Soria A, Lortholary O, Stanbury T, Bouquillon B, Sauvage C, Javier RM, Hermine O, Arock M, CEREMAST Network.   +15 more
europepmc   +2 more sources

Cutaneous Mastocytosis in Children: Is It Just a Skin Disease?

Çocuk Dergisi, 2021
Introduction: Mastocytosis is characterized by the excessive proliferation and accumulation of mast cells in organs such as the spleen, liver, lymph nodes, skin, gastrointestinal tract, and bone marrow.
Tuğba Aktürk, Emine Türkkan, Deniz Özçeker   +2 more
doaj   +1 more source

Systemic Lymphadenopathic Mastocytosis with Eosinophilia

Diagnostics, 2022
Systemic mastocytosis is a neoplastic proliferation of mast cells that most frequently involves cutaneous sites. Mastocytosis involves various extracutaneous sites, but the lymph node is rare.
Soyoung Im, Jeong-A Kim, Gyeongsin Park, Uiju Cho   +3 more
doaj   +1 more source

Phenotypic and genotypic characteristics of mastocytosis according to the age of onset. [PDF]

, 2008
International audienceAdult's mastocytosis is usually associated with persistent systemic involvement and c-kit 816 mutation, while pediatrics disease is mostly limited to the skin and often resolves spontaneously.
A Iemura, AC Garcia-Montero, Adeline Catteau, Alain Moussy, Annick Cohen-Akenine, AS Worobec, Beatrix Sans, BJ Longley Jr., BM Czarnetzki, C Buttner, Christine Bodemer, Cédric Baude, Danièle Canioni, David Ghez, David M. Ojcius, Fabienne Palmerini, Fanny Lanternier, Felipe Suarez, Frédéric Feger, Frédérique Soppelsa, H Nagata, H Yanagihori, Hagay Sobol, HP Horny, Jean Marie Launay, JM Azana, K Hartmann, K Hartmann, Katia Hanssens, L Escribano, LA Fearfield, LY Zhang, MA Middelkamp Hup, Michel Arock, OE Rodermund, Olivier Hermine, Olivier Lortholary, P Valent, P Valent, Patrice Dubreuil, Philippe Casassus, Richard Delarue, S Fraitag-Spinner, Stéphane Barète, Sylvie Fraitag, T Furitsu, YA Mekori, Yael Zermati, Ying Yang   +48 more
core   +14 more sources

Pseudoxanthomatous diffuse cutaneous mastocytosis in a child [PDF]

Journal of Krishna Institute of Medical Sciences University, 2023
Abnormal accumulation of mast cells in the skin is called cutaneous mastocytosis. Diffuse cutaneous mastocytosishas two clinical variants, pseudoxanthomatous/xanthelasmoid and bullous type. Childhood disease is mostly self limiting. This may sometimes be
Ritu Gujarati Vishwanath, Ramesh Vishwanath, Varun Vishwanath   +2 more
doaj  

Urticaria pigmentosa and systemic mastocytosis

Clinical Case Reports, 2023
Key Clinical Message Additional investigations for systemic involvement should be initiated once the diagnosis of cutaneous mastocytosis has been established in an adult patient.
Jonathan Keow, Benjamin Chin‐Yee, Cyrus C. Hsia, Kara Robertson   +3 more
doaj   +1 more source

Diffuse cutaneous mastocytosis masquerading as linear IgA bullous dermatosis of childhood

Dermatology Reports, 2021
Diffuse cutaneous mastocytosis is a rare form of cutaneous mastocytosis that can appear in heterogeneous clinical presentations, including eruption of papules, erythematous plaques, blisters, and erythroderma.
Tuntas Rayinda, Dyah Ayu Mira Oktarina, Retno Danarti   +2 more
doaj   +1 more source

Differential Diagnoses of Systemic Mastocytosis in Routinely Processed Bone Marrow Biopsy Specimens: A Review [PDF]

, 2010
Diagnosis of systemic mastocytosis (SM) is mainly based on the morphological demonstration of compact mast cell infiltrates in various tissue sites. In almost all patients such infiltrates are detected in the bone marrow.
Horny, H. -P., Sotlar, K., Valent, P.
core   +1 more source

Diffuse cutaneous mastocytosis in an infant

Indian Journal of Paediatric Dermatology, 2016
Mastocytosis is a group of a disorder characterized by infiltration of mast cell in various organs, e.g. skin, bone marrow, liver, spleen, gastrointestinal tract, lymph node, etc., The term bullous mastocytosis is generally used to describe the varieties
Sitangshu Chatterjee, Satarupa Mukherjee, Malay Kumar Sinha   +2 more
doaj   +1 more source

Bullous disease in infant: think of cutaneous mastocytosis

PAMJ Clinical Medicine, 2020
Mastocytosis is a rare disease. The cutaneous form is the most frequent. There are several clinical forms of cutaneous mastocytosis including the bullous form which is rare.
Kaoutar Achehboune, Khadija Elboukhari, Hanane Baybay, Sara Elloudi, Fatima Zahra Mernissi   +4 more
doaj   +1 more source