Results 71 to 80 of about 10,225 (204)

Maculopapular Cutaneous Mastocytosis Successfully Treated with Omalizumab

, 2021
Maculopapular cutaneous mastocytosis (MPCM), formerly telangiectasia macularis eruptiva perstans (TMEP), is an uncommon form of cutaneous mastocytosis first described on 1930 (1).
Kanni, Theodora, Tampouratzi, Eleftheria, Douvali, Theodora, Katsantonis, John   +3 more
core  

Generalized Blistering in Infancy: A Rare Case Report on Bullous Mastocytosis

Nepal Journal of Dermatology, Venereology & Leprology
Mastocytosis is a rare myeloid neoplasm characterized by abnormal proliferation of mast cells, associated with c-KIT mutations. The disease is most frequently observed in childhood, with clinical presentations ranging from solitary mastocytoma to diffuse
Aditi Haldar, Bhagyashree Supekar, Vishwajeet Mande, Jayesh Mukhi   +3 more
doaj   +1 more source

Mastocytosis in Children: Literature Review and Own Clinical Observation

Zdorovʹe Rebenka, 2013
The review of literature presents the data on neoplastic disease — mastocytosis. We provide the modern information of the etiopathogenesis, classification, clinical presentation, methods of diagnosis and treatment in children. We presented own experience
N.V. Nagornaya, Ye.V. Bordyugova, A.P. Koval, A.V. Dubovaya   +3 more
doaj   +1 more source

Cutaneous mastocytosis: Two pediatric cases treated with topical pimecrolimus. [PDF]

, 2010
Cutaneous mastocytosis is characterized by increased numbers of skin mast cells that release mediators causing pruritus, urticaria, and flushing. Most pediatric mastocytosis patients exhibit the pattern of urticaria pigmentosa, which typically appears ...
Correia, Osvaldo, Correia, O, Delgado, L, Duarte, Ana Filipa, Quirino, Paula, Delgado, Luis, Duarte, AF, Quirino, P, Azevedo, R, Azevedo, Rosa   +9 more
core   +1 more source

Urticaria pigmentosa: A case report

Nepal Journal of Dermatology, Venereology & Leprology, 2016
Mastocytosis is a heterogenous group of diseases characterized by abnormal infiltration of mast cells in the skin and other organs. Urticaria Pigmentosa is the most common variant of cutaneous mastocytosis.
Mohammad Abid Keen
doaj   +3 more sources

Imatinib Mesylate in the Treatment of Diffuse Cutaneous Mastocytosis

, 2013
Diffuse cutaneous mastocytosis is a less common but potentially life-threatening variant of childhood mastocytosis. Here we report 2 children with diffuse cutaneous mastocytosis in whom an activating somatic KIT mutation was detected.
Renard, Marleen, Dubreuil, Patrice, Debiec-Rychter, Maria, Martin, Ludovic, Hoppé, Anne, Uyttebroeck, Anne, Morren, Marie-Anne   +6 more
core   +1 more source

Diffuse erythroderma cutaneous mastocytosis with bone marrow infiltration

, 1993
We report a case of diffuse crythrodcrmic cutaneous mastocytosis with bone marrow infiltration. An 11-month-old female patient was referred to our hospital for intermittent flushing, fever, intense itching, erythematous rash and bullous lesions ...
Çevik, N., Ören, B., ÖREN, HALE, POLAT, MEHMET AKİF, İrken, G., Olgun, Nur   +5 more
core   +1 more source

[Cutaneous mastocytosis - update and clinical guidelines]

, 2018
Mastocytosis is a rare and multifaceted disease group characterized by mast cell accumulation in the skin and/or internal organs. In its most common form solitary or widespread, often itchy, red-brown skin lesions appear in childhood or during adulthood (
Rollman, O, Nilsson, G,, Emtestam, L,, Mattson, M, Hägglund, H, Bergström, A, Karlsson, M   +6 more
core  

Pseudoangiomatous xanthelasmoid mastocytosis: Two case reports showing the hypervascularity of this rare variant of cutaneous mastocytosis

, 2016
Xanthelasmoid mastocytosis or xanthelasmoidea is a rare clinical variant of cutaneous mastocytosis characterized by a yellow hue of the clinical lesions, which are often misdiagnosed as juvenile xanthogranuloma.
Kolivras, Athanassios, Thompson, Curtis T, André, Josette, Sass, Ursula, Fraitag, Sylvie   +4 more
core   +1 more source

Case Report - Cutaneous mastocytosis: Report of six cases

, 2006
Cutaneous mastocytosis is a rare infiltrative disorder of the skin. Though often asymptomatic, systemic features may be associated with any clinical pattern of the disorder at any age group.
Arun C. Inamadar, Aparna Palit
core   +1 more source