Results 71 to 80 of about 177,875 (202)

Cutaneous Mastocytosis

Liječnički vjesnik
Cutaneous mastocytosis is a rare disorder characterized by the proliferation and accumulation of abnormal mast cells in the skin, without evidence of internal organ involvement. It represents the most common form of mastocytosis in childhood, whereas in adult patients cutaneous manifestations often indicate the presence of systemic disease.
Catarina Martins, Ines Vivas, Maria Jose Dinis   +2 more
  +4 more sources

Solitary mastocytoma presenting in an adult: report and literature review of adult-onset solitary cutaneous mastocytoma with recommendations for evaluation and treatment

Dermatology Practical & Conceptual, 2016
Background: Mastocytosis is either cutaneous (with skin-limited proliferation of mast cells) or systemic (with mast cells in extracutaneous sites). The onset of solitary mastocytoma in an adult is rare.
Philip R. Cohen
doaj   +1 more source

Diagnostic Accuracy of Tests for Hymenoptera Venom Hypersensitivity: A Systematic Review and Bayesian Meta‐Analysis Protocol

Health Science Reports, Volume 9, Issue 7, July 2026.
ABSTRACT Background and Aims Hymenoptera venom hypersensitivity is a potentially life‐threatening condition that may affect up to 7.5% of adults worldwide and can result in systemic allergic reactions ranging from generalized cutaneous symptoms to severe anaphylaxis.
Bharat Kumar, Madalyn Walsh, Amir Abidov, Melissa Swee   +3 more
wiley   +1 more source

Diffuse cutaneous mastocytosis with generalized bullae [PDF]

, 2010
We report on a 9-month-old female infant with multiple tense bullae and erosions covering the entire body, including the face, scalp, and trunk. The histopathological examination revealed sub-epidermal bullae with a dense dermal cellular infiltrate.
김수찬
core   +1 more source

European S2k guidelines on management of autoimmune blistering diseases in children and adolescents

Journal of the European Academy of Dermatology and Venereology, Volume 40, Issue 7, Page 1137-1161, July 2026.
Autoimmune blistering disorders (AIBDs) in children are rare, challenging to diagnose and treat and often require immunosuppressants. Until now, no paediatric care guidelines existed. The EADV Task Force for AIBDs has developed the consensus‐based recommendations, enabling physicians to adopt a uniform, tailored treatment strategy to improve outcomes ...
A. Nanda, B. Tedbirt, C. Bodemer, M. C. Bolling, M. El Hachem, M. Nikolić, E. Benton, M. Caproni, D. De, D. Didona, K. Drenovska, M. Goebeler, M. Hertl, B. Horváth, M. Kasperkiewicz, D. Kiritsi, M. Larralde, A. V. Marzano, J. Meijer, D. F. Murrell, J. Powell, E. Sprecher, N. S. Chandran, M. M. Tomayko, S. Uzun, N. van Beek, H. Ott, A. Patsatsi, A. Torrelo, A. Welfringer‐Morin, E. Schmidt, P. Joly   +31 more
wiley   +1 more source

Imatinib Mesylate in the Treatment of Diffuse Cutaneous Mastocytosis

, 2013
Diffuse cutaneous mastocytosis is a less common but potentially life-threatening variant of childhood mastocytosis. Here we report 2 children with diffuse cutaneous mastocytosis in whom an activating somatic KIT mutation was detected.
Renard, Marleen, Dubreuil, Patrice, Debiec-Rychter, Maria, Martin, Ludovic, Hoppé, Anne, Uyttebroeck, Anne, Morren, Marie-Anne   +6 more
core   +1 more source

Breakthrough reactions in pediatric chemotherapeutic desensitization: Outcomes and associated risk factors

Pediatric Allergy and Immunology, Volume 37, Issue 7, July 2026.
Breakthrough reactions in Pediatric chemotherapeutic desensitization: outcomes and associated risk factors. Abstract Background Rapid drug desensitization (RDD) enables the safe reintroduction of chemotherapeutic agents in patients with hypersensitivity reactions (HSRs).
Pathitta Doradee, Supaluk Tangvalelerd, Kantima Kanchanapoomi, Prapasri Kulalert, Punchama Pacharn, Orathai Jirapongsananuruk, Witchaya Srisuwatchari   +6 more
wiley   +1 more source

Maculopapular Cutaneous Mastocytosis Successfully Treated with Omalizumab [PDF]

, 2021
Maculopapular cutaneous mastocytosis (MPCM), formerly telangiectasia macularis eruptiva perstans (TMEP), is an uncommon form of cutaneous mastocytosis first described on 1930 (1).
Kanni, Theodora, Tampouratzi, Eleftheria, Douvali, Theodora, Katsantonis, John   +3 more
core   +1 more source

Drug hypersensitivity reactions and allergy in patients with mastocytosis [PDF]

, 2017
Mastocytosis is a rare myeloproliferative disease caused by excessive proliferation and accumulation of mast cells in the skin and internal organs. The most common variant of mastocytosis in children is cutaneous mastocytosis.
Barbara Kwiecińska, Roman Nowicki, Hanna Ługowska-Umer, Justyna H. Czarny, Marek B. Niedoszytko, Monika Sikorska, Magdalena Lange, Aleksandra Górska   +7 more
core   +1 more source

Generalized Blistering in Infancy: A Rare Case Report on Bullous Mastocytosis

Nepal Journal of Dermatology, Venereology & Leprology
Mastocytosis is a rare myeloid neoplasm characterized by abnormal proliferation of mast cells, associated with c-KIT mutations. The disease is most frequently observed in childhood, with clinical presentations ranging from solitary mastocytoma to diffuse
Aditi Haldar, Bhagyashree Supekar, Vishwajeet Mande, Jayesh Mukhi   +3 more
doaj   +1 more source