Results 81 to 90 of about 12,161 (224)
Childhood Pseudoxanthomatousmastocytosis; Report of two cases
Cutaneous mastocytosis (CM) is a mast cell proliferative disorder that commonly affects pediatric population. It has various clinical forms such as urticaria pigmentosa, solitary mastocytoma, telangiectasia macularis eruptiva perstans, diffuse CM, and ...
Bhabani S. T. P. Singh +3 more
doaj +1 more source
Systemic mastocytosis (SM) with associated hematological neoplasia (SM‐AHN) is a rare and aggressive condition characterized by abnormal clonal proliferation of mast cells and the concurrent occurrence of hematologic malignancies, such as acute myeloid leukemia (AML).
Sona Vardanyan +6 more
wiley +1 more source
Generalized Blistering in Infancy: A Rare Case Report on Bullous Mastocytosis
Mastocytosis is a rare myeloid neoplasm characterized by abnormal proliferation of mast cells, associated with c-KIT mutations. The disease is most frequently observed in childhood, with clinical presentations ranging from solitary mastocytoma to diffuse
Aditi Haldar +3 more
doaj +1 more source
Systemic Mastocytosis - a Diagnostic Challenge [PDF]
Mastocytosis refers to a group of disorders characterized by the infiltration of clonally derived mast cells to the skin or extracutaneous tissues resulting in a heterogeneous clinical picture. It is a rare hematologic disorder in all its forms.
Galzerano, A +3 more
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Urticaria pigmentosa: A case report
Mastocytosis is a heterogenous group of diseases characterized by abnormal infiltration of mast cells in the skin and other organs. Urticaria Pigmentosa is the most common variant of cutaneous mastocytosis.
Mohammad Abid Keen
doaj +3 more sources
Mastocytosis in Children: Literature Review and Own Clinical Observation
The review of literature presents the data on neoplastic disease — mastocytosis. We provide the modern information of the etiopathogenesis, classification, clinical presentation, methods of diagnosis and treatment in children. We presented own experience
N.V. Nagornaya +3 more
doaj +1 more source
Exercise-induced anaphylaxis: an update [PDF]
Exercise-induced anaphylaxis (EIAn) is a rare and potentially fatal syndrome associated with exercise. It is the most serious and potentially life-threatening hypersensitivity phenomenon for athletes of all sports.
Del Giacco, Stefano
core +1 more source
Cutaneous Mastocytosis in Childhood. Retrospective Study of 32 Patients [PDF]
Introdução: A designação de mastocitose engloba várias entidades clinicamente distintas caracterizadas pela acumulação tissular de mastócitos. A pele é o órgão mais frequentemente envolvido.
Amaro, C +4 more
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Targeting phosphatidylinositol-3-kinase pathway for the treatment of Philadelphia-negative myeloproliferative neoplasms [PDF]
Myeloproliferative neoplasms (MPN) are a diverse group of chronic hematological disorders that involve unregulated clonal proliferation of white blood cells.
Kapur, Reuben, Pandey, Ruchi
core +1 more source

