Results 21 to 30 of about 20,747 (199)
Iron-based nanocatalyst for the acceptorless dehydrogenation reactions
Nature Communications, 2017 Catalytic acceptorless dehydrogenation reactions provide a sustainable route to valuable products and hydrogen fuel. Here, the authors show a recyclable iron catalyst that is highly active in the acceptorless dehydrogenation of a wide range of N ...
Garima Jaiswal +3 more
doaj +1 more source
Experiencias y prototipos de aplicaciones de TV Digital interactivas
Informes Científicos y Técnicos (Universidad Nacional de la Patagonia Austral), 2014 La TV Digital es una tecnología, que va a transformar la experiencia de ver televisión. Imagen y sonido en alta definición junto con la interactividad son posibles gracias al pasaje de la transmisión analógica a la digital, la cual permite enviar datos ...
Fernanda Daniela Oyarzo +3 more
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Microbiology Spectrum, 2022 Seneca Valley virus (SVV) is a recently discovered pathogen that poses a significant threat to the global pig industry. It has been shown that many viruses are reliant on nucleocytoplasmic trafficking of nucleolin (NCL) for their own replication.
Jiangwei Song +3 more
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Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease, 2013 Despite the identification of a large number of disease-causing genes in recent years, it is still unclear what disease mechanisms operate in the neuronal ceroid lipofuscinoses (NCLs, Batten disease). As a group they are defined by the specific accumulation of protein, either subunit c of mitochondrial ATP synthase or SAPs A and D in lysosome-derived ...
Palmer, DN +3 more
openaire +3 more sources
Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease, 2015 The neuronal ceroid lipofuscinoses (NCL) currently encompass fourteen genetically different forms, CLN1 to CLN14, but are all morphologically marked by loss of nerve cells, particularly in the cerebral and cerebellar cortices, and the cerebral and extracerebral formation of lipopigments.
Radke, Josefine +2 more
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Pharmacological approaches to tackle NCLs
Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease, 2020 Neuronal ceroid lipofuscinoses, also collectively known as Batten disease, are a group of rare monogenic disorders caused by mutations in at least 13 different genes. They are characterized by the accumulation of lysosomal storage material and progressive neurological deterioration with dementia, epilepsy, retinopathy, motor disturbances, and early ...
Kauss V. +2 more
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Angewandte Chemie, EarlyView.Peptide‐to‐Small Molecule Paradigm: Peptidomimetics have evolved from simple mimicry toward drug‐like scaffolds supported by increasing clinical successes. This Perspective highlights the geometric design principles—linear repetition, convergent fusion, and cyclization—defining the next‐generation peptidomimetic architectures capable of targeting ...
Jesang Lee +5 more
wiley +2 more sources
Revue d’Elevage et de Médecine Vétérinaire des Pays Tropicaux, 1997 Une typologie des élevages de cerfs a été réalisée grâce à la méthode graphique de Bertin. Quatre grands types d'élevage qui se différenciaient essentiellement selon la superficie des pâturages, le chargement moyen et l'intensification des pratiques d ...
Sébastien Le Bel +2 more
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Asynchronous Register Less NULL Convention Logic (RL-NCL) Pipeline Architectures Using Basic Gates
Memoria Investigaciones en Ingeniería, 2022 Asynchronous circuits is an alternative to design digital systems that is becoming the interest of many researchers in the digital design area mainly due to it’s low-power consumption and robustness.
Gabriel C. Duarte, Duarte L. Oliveira
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NCL diseases — clinical perspectives
Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease, 2013 The neuronal ceroid lipofuscinoses (NCLs) are lysosomal storage disorders and together are the most common degenerative brain diseases in childhood. They are a group of disorders linked by the characteristic accumulation of abnormal storage material in neurons and other cell types, and a degenerative disease course.
Schulz A. +4 more
openaire +2 more sources