Results 91 to 100 of about 1,645,101 (196)

Exceptional Clinical Response to Surgery in Somalian Child Affected by Hyper Secretive Adrenal Cortical Carcinoma

International Medical Case Reports Journal, 2022
Ahmed Adam Osman,1 Ahmed Omar Abdi,2 Ismail Mohamud Abdullahi,3 Mehmet Tahtabasi,4 Veysel Kaya5 1Department of Radiology, University of Health Sciences-Somalia Turkey Recep Tayyip Erdogan Education and Research Hospital, Mogadishu, Somalia; 2Department ...
Osman AA, Omar Abdi A, Mohamud Abdullahi I, Tahtabasi M, Kaya V   +4 more
doaj  

Feminizing adrenocortical tumors: Literature review

Indian Journal of Endocrinology and Metabolism, 2015
Feminizing adrenal tumors (FAT) are extremely rare tumors prevailing in males. Clinical manifestations are gynecomastia and/or other hypogonadism features in adults. They are rarer in pediatric population and their main manifestation is peripheral sexual
Farida Chentli, Ilyes Bekkaye, Said Azzoug   +2 more
doaj   +1 more source

Clinical, Genetic, and Prognostic Features of Adrenocortical Tumors in Children: A 10-Year Single-Center Experience

Frontiers in Oncology, 2020
Background and Aims: Pediatric adrenocortical tumors (ACTs) are very rare endocrine neoplasms in childhood. In this study, we performed a retrospective analysis of children with ACT treated at our institution by examining clinical and genetic disease ...
Evelina Miele, Angela Di Giannatale, Alessandro Crocoli, Raffaele Cozza, Annalisa Serra, Aurora Castellano, Antonella Cacchione, Maria Giuseppina Cefalo, Rita Alaggio, Maria Debora De Pasquale   +9 more
doaj   +1 more source

Multidisciplinary Tumor Board Evaluation of Pediatric Patients with Adrenocortical Tumors Across Seven International Centers

Cancers
Background: The management of rare tumors at reference centers with specialized multidisciplinary tumor boards (MTBs) improves patient survival. No international standardized diagnostic and treatment recommendations for pediatric patients with adrenocortical carcinoma (ACC) exist so far.
Maria Riedmeier, Wiebke Schlötelburg, Shipra Agarwal, Ahitagni Biswas, Saniye Ekinci, Martin Fassnacht, Maria C. B. Villares Fragoso, E. Nazli Gonc, Melis Gultekin, Mithat Haliloglu, Vishesh Jain, Manisha Jana, Dominika Janus, Jagdish Prasad Meena, Jessica Munarin, Diclehan Orhan, Jaydira Del Rivero, Rajni Sharma, Gerdi Tuli, Bilgehan Yalcin, Verena Wiegering   +20 more
openaire   +5 more sources

Adrenocortical carcinoma in a pediatric patient with li-fraumeni-like Syndrome: an endemic condition in southern Brazil

Clinical and Biomedical Research, 2021
A 12-year-old boy with germline TP53-R337H mutation and family history of early adrenocortical carcinoma (ACC) was admitted to hospital with abdominal pain and distention.
Mariana Mendes Knabben, Renan Reis Caldas, Jéssica Onofre de Brito Lima, Aline Spader Casagrande, Caroline Lorenzoni Almeida Ghezzi   +4 more
doaj  

Adrenocortical Tumors in Pediatrics beyond the Classic Presentation: A Case Series

Hormone Research in Paediatrics
Introduction: Adrenocortical tumors (ACTs) are rare pediatric malignancies, typically presenting with signs of virilization or hypercortisolism. However, nonclassical presentations may delay diagnosis and complicate management. Our study aimed to illustrate the diagnostic and therapeutic challenges posed by atypical forms of pediatric ACTs through a ...
Elsa Dieterlen, Carine Villanueva, Sara Cabet, Grégoire Schneider, Cécile Picard, Marc Nicolino, Cecile Faure-Conter, Kevin Perge   +7 more
openaire   +1 more source

Mitotane Associated With Cisplatin, Etoposide, And Doxorubicin In Advanced Childhood Adrenocortical Carcinoma: Mitotane Monitoring And Tumor Regression

, 2015
PURPOSE: To define a mitotane dose for pediatric patients with adrenocortical cancer (ACC) that maintains therapeutic plasma levels (TL) between 14 and 20 μg/mL and to verify its antitumor efficacy in association with 8 cycles of cisplatin, etoposide ...
Parise G.A., Callefe L.G., Zancanella P., Santana M.H.A., Oliveira B.H., Pianovski M.A.D., Voss S.Z., Piovezan G.C., Figueiredo B.C., Ferman S., Stinghen S.T., Lichtvan L.L.   +11 more
core   +1 more source

Silent Corticotroph Tumor with Adrenocortical Choristoma in an Eleven-year-old Boy

, 2022
Silent corticotroph tumors are composed of corticotroph cells, but do not manifest any biochemical or clinical evidence of hypercortisolism. A choristoma is a benign, congenital proliferation of histologically mature tissue elements normally not present ...
ERCAN, OYA, EVLİYAOĞLU, SAADET OLCAY, Tarcin, Gurkan, Mete, Ozgur, TURAN, Hande, Sinoplu, Ada Bulut, ÖZ, AYŞİM BÜGE   +6 more
core   +1 more source

Low Expression of HLA-DRA, HLA-DPA1, and HLA-DPB1 is Associated With Poor Prognosis in Pediatric Adrenocortical Tumors (ACT)

, 2014
BackgroundLow expression of HLA class II antigens has been associated with more aggressive disease in several human malignancies including adult adrenocortical tumors (ACT), but their clinical relevance in pediatric ACT needs to be investigated ...
Leandra N. Z. Ramalho, Neder, Luciano, Silvio Tucci, Ana L. Seidinger, Lira, Regia C. P., Tucci, Silvio, Scrideli, Carlos A., Seidinger, Ana L., Fabíola A. Leite, Luciano Neder, Cardinalli, Izilda A., Silvia R. Brandalise, José A. Yunes, Carlos E. Martinelli, Mastelaro, Maria J., Sonir R. R. Antonini, Regia C. P. Lira, Fedatto, Paola F., Tone, Luiz G., Luiz G. Tone, Yunes, Jose A., Castro, Margaret de, Antonini, Sonir R. R., Maria J. Mastelaro, Carlos A. Scrideli, Leite, Fabiola A., Brandalise, Silvia R., Ramalho, Leandra N. Z., Margaret de Castro, Paola F. Fedatto, Izilda A. Cardinalli, Martinelli, Carlos E.   +31 more
core   +1 more source

Pediatric Adrenocortical Carcinoma: The Nuts and Bolts of Diagnosis and Treatment and Avenues for Future Discovery [PDF]

Allison F O’Neill,1 Raul C Ribeiro,2 Emilia M Pinto,3 Michael R Clay,4 Gerard P Zambetti,3 Brent A Orr,3 Christopher B Weldon,5 Carlos Rodriguez-Galindo2,6 1Department of Pediatric Oncology, Dana-Farber/Boston Children’s Cancer and Blood Disorders Center,
Zambetti GP, O'Neill AF, Ribeiro RC, Weldon CB, Orr BA, Rodriguez-Galindo C, Pinto EM, Clay MR   +7 more
core