Results 91 to 100 of about 710,498 (297)

Hereditary periodic fever syndromes [PDF]

, 2012
Hereditary periodic fever syndromes, comprise a group of hereditary disorders with similar clinical features of recurrent short episodes of fever associated with inflammatory manifestations.
Shawky, RM, Gaboon, NEA
core  

Impaired Fibrinolysis in the Pathogenesis of Dengue Hemorrhagic Fever [PDF]

, 2002
The mechanisms contributing to bleeding complications in dengue hemorrhagic fever were studied by investigating the pattern of activation of the coagulation and fibrinolytic systems in 50 children with severe dengue hemorrhagic fever.
Eric C.M. van Gorp, ten Cate, H, Brandjes, DPM, Wil M.V. Dolmans, van der Meer, Jos W. M., Mairuhu, Albert T. A., Cate Ht, Hugo ten, Mairuhu, A.T., Brandjes, D.P., Cate, H.H., Setiati, T.E., Dolmans, W.M.V., Jos W.M. van der Meer, Hugo ten Cate, Hack, C. Erik, Hack, C.E., Mairuhu, ATA, Cate, H. ten, C. Erik Hack, Suharti, C., Catharina Suharti, Gorp, E. van, Brandjes, D.P.M., Albert T.A. Mairuhu, Dolmans, Wil M. V., Meer, J.W.M. van der, Setiati, Tatty E., Mairuhu, A.T.A., Tatty E. Setiati, Suharti, Catharina, Dees P.M. Brandjes, van Gorp, Eric C. M., Gorp, E.C.M. van, Brandjes, Dees P. M.   +33 more
core   +1 more source

Clinical Characteristics and Concordance of Anti‐MDA5 Antibodies: A Multicenter Australian Study

Arthritis Care &Research, EarlyView.
Objective In Australia, anti‐MDA5 antibodies are exclusively tested by a line immunoblot assay (LIA). The clinical concordance of an LIA‐positive anti‐MDA5 result is unclear. We aimed to describe the clinical features and determine the clinical concordance of patients with anti‐MDA5 antibodies. Methods Electronic records of a multisite cohort (patients
Syed B. Ali, Thomas Khoo, Keeran Shivakumar, Adam Caroll, Lauren Hender, Dimitra Beroukas, Kim Griggs, Celina Jin, Theo De Malmanche, Jessica Day, Gabor Major, Vidya Limaye   +11 more
wiley   +1 more source

Periodic fever syndromes in Eastern and Central European countries: results of a pediatric multinational survey

Pediatric Rheumatology Online Journal, 2010
Objective To analyze the prevalence of diagnosed and suspected autoinflammatory diseases in Eastern and Central European (ECE) countries, with a particular interest on the diagnostic facilities in these countries.
Stefan Mariana, Harjaček Miroslav, Wolska-Kuśnierz Beata, Čižnar Peter, Pašić Srdjan, Sedivà Anna, Constantin Tamas, Dolezalovà Pavla, Toplak Nataša, Ruperto Nicolino, Gattorno Marco, Avčin Tadej   +11 more
doaj   +1 more source

Computation of Kalman Decompositions of Periodic Systems [PDF]

, 2003
We consider the numerically reliable computation of reachability and observability Kalman decompositions of a periodic system with time-varying dimensions.
A. Varga, Andras Varga, Varga, A., Varga, Andras   +3 more
core   +1 more source

Incidence, Risk Factors and Management of Adverse Events in Contemporary Real‐World Care of Children with Juvenile Idiopathic Arthritis

Arthritis Care &Research, Accepted Article.
Objective We describe the frequency, risk factors, severity, and management of actionable and serious adverse events (AAE and SAE) in children with newly diagnosed Juvenile Idiopathic Arthritis (JIA) in Canada. Methods We enrolled patients within 3 months of JIA diagnosis in the Canadian Alliance of Pediatric Rheumatology Investigators (CAPRI) Registry,
Bashayer Alnuaimi, Roberta A. Berard, Jean‐Philippe Proulx‐Gauthier, Heinrike Schmeling, Michelle Batthish, Gilles Boire, Adam M. Huber, Dax G. Rumsey, Jaime Guzman, Gaëlle Chédeville, The CAPRI registry Investigators   +10 more
wiley   +1 more source

CD70 Deficiency due to a Novel Mutation in a Patient with Severe Chronic EBV Infection Presenting As a Periodic Fever

Frontiers in Immunology, 2018
Primary immunodeficiencies with selective susceptibility to EBV infection are rare conditions associated with severe lymphoproliferation. We followed a patient, son of consanguineous parents, referred to our center for recurrent periodic episodes of ...
Roberta Caorsi, Marta Rusmini, Stefano Volpi, Sabrina Chiesa, Claudia Pastorino, Angela Rita Sementa, Paolo Uva, Alice Grossi, Edoardo Lanino, Maura Faraci, Francesca Minoia, Sara Signa, Paolo Picco, Alberto Martini, Isabella Ceccherini, Marco Gattorno   +15 more
doaj   +1 more source

Engineering Approaches to Modify Immunomodulatory Functions of Mesenchymal Stromal Cells (MSCs): Tissue Regeneration and Clinical Application

Advanced Science, EarlyView.
Mesenchymal stromal cells (MSCs) show promise for treating immune‐related disorders through immunomodulation and tissue regeneration. This review gives a brief overview of current clinical approval of MSC therapies. It also discussed how bioengineering, including genetic modification, biomaterial delivery, extracellular vesicles, and iPSC‐derived MSCs,
Sichen Yang, Kejia Li, Ning Wang, Zhen Li, Zhiyong Zhang, Rocky S. Tuan, Yangzi Jiang   +6 more
wiley   +1 more source

How to identify a patient with autoinflammatory syndrome: Clinical and diagnostic algorithms

Современная ревматология, 2013
Autoinflammatory syndromes (AISs) are a group of predominantly hereditary diseases associated with the spontaneous uncontrolled production of proinflammatory cytokines. Most diseases are known to have molecular mechanisms and an inheritance pattern.
Mikhail Mikhailovich Kostik, L S Snegireva, M F Dubko, V V Masalova, T S Likhacheva, O V Kalashnikova, V G Chasnyk   +6 more
doaj   +1 more source

The Genetic Basis for Periodic Fever [PDF]

The American Journal of Human Genetics, 1999
The periodic-fever syndromes are a genetically heterogeneous group of inflammatory disorders characterized by recurrent fever, abdominal pain, and polyserositis. The clinically distinct entities of familial Mediterranean fever (FMF; MIM 249100) and hyperimmunoglobulinemia D with periodic fever (MIM 260920) are autosomal recessive and genetically ...
openaire   +2 more sources