Results 71 to 80 of about 42,983 (297)

The etiological spectrum of pediatric FUO and clinical management of PFAPA/SURF: a ten-year retrospective study

Frontiers in Immunology
BackgroundThis study aimed to define the etiologies and clinical features of pediatric Fever of unknown origin (FUO), focusing on periodic fever, aphthous stomatitis, pharyngitis, and cervical adenitis (PFAPA) and the syndrome of undifferentiated ...
Chenchen Guan, Qinhua Zhou, Jinqiao Sun, Wenjing Ying, Xiaoying Hui, Jia Hou, Lipin Liu, Chenghao Wang, Luyao Liu, Bijun Sun, Wenjie Wang, Xiaochuan Wang, Xiaochuan Wang   +12 more
doaj   +1 more source

Transitional care management in patients with auto-inflammatory diseases: experience of cooperation of a paediatric and adult centre

Journal of Transition Medicine, 2022
Auto-inflammatory Diseases (AIDs) are a group of diseases with a strong genetic component, inducing an inappropriate activation of innate immunity. The patients with pediatric onset will face the transitional care (TC) from a pediatrician to an adult ...
Soscia Francesca, Sicignano Ludovico Luca, Verrecchia Elena, Ardenti Morini Francesca, Massaro Maria Grazia, Civitelli Fortunata Sabrina, Ferrari Federica, Rigante Donato, Cortis Elisabetta, Manna Raffaele   +9 more
doaj   +1 more source

Hereditary periodic fever syndromes

, 2011
Hereditary periodic fever syndromes, comprise a group of hereditary disorders with similar clinical features of recurrent short episodes of fever associated with inflammatory manifestations.
Shawky, Rabah M., Gaboon, Nagwa E.A., Nagwa E.A. Gaboon, Rabah M. Shawky   +3 more
core   +1 more source

Discordance Between Systemic Lupus Erythematosus Disease Activity Index Domain Weights and Their Association With Organ Damage Accrual

Arthritis Care &Research, EarlyView.
Objective Studies of damage accrual in patients with systemic lupus erythematosus (SLE) show associations with disease activity measured by the SLE Disease Activity Index 2000 (SLEDAI‐2K), but these associations are imperfect. SLEDAI scores are powerfully influenced by weightings (1–8) assigned to each domain.
Kevin Zhang, Eric F. Morand, Sarah E. Boyd, François Petitjean, Alberta Hoi, Rachel Koelmeyer, Iolanda Miceli, Julie A. Monk, Hieu T. Nim   +8 more
wiley   +1 more source

Familial Mediterranean fever in northwest of Iran (Ardabil): The first global report from Iran [PDF]

Familial Mediterranean fever (FMF), which is the prototype of the hereditary periodic fever syndromes, is common in the countries around the Mediterranean Sea. Considering its geographical position in the northwest of Iran, with its population of Turkish
فیضی, ایرج, خلفی, جعفر, صالح زاده, فرهاد, عظیمی, هرمز, ذولفقاری, علی اصغر, براک, منوچهر, جستان, مارینا, حبیب زاده, شهرام, امامی, دینا, یزدانبد, عباس, بشردوست, بهمن   +10 more
core  

Biomarkers in children with periodic fever syndromes [PDF]

, 2016
- 4 - Abstract Introduction: Periodic fever syndromes are clinical entities classified as autoinflammatory diseases. The most of the periodic fever syndromes have genetic predisposition (monogenic periodic fever syndromes). PFAPA (Periodic Fever, Aphtous
Król, Petra
core  

PERIODIC DISEASE (FAMILIAL MEDITERRANEAN FEVER) IN CHILDREN

, 2017
The article provides modern approaches to etiopathogenesis, diagnostics and therapy of the familial Mediterranean fever (periodic disease) in children, clinical and genetic aspects of the disease are ...
G. G. Amaryan
core   +1 more source

[Recurrent febrile episodes--normal, periodic fever syndrome or immunodeficiency?]

, 2006
Fever is one of the main symptoms leading to medical evaluation. Not only infections cause fever but also inflammatory disorders. To distinguish one from another, a thorough medical history and clinical evaluation are needed. Sometimes, only the clinical
Duppenthaler, A
core  

Marburg Virus Glycoprotein Is a Remarkable Virulent Factor Linked to Hemorrhagic Pathology: Evidence from Multimodal Experimental Systems

Advanced Science, EarlyView.
By integrating data from in vitro, ex vivo, and in vivo models, our research identifies the MARV glycoprotein as a remarkable hemorrhagic factor, filling a major gap in this important field. It also provides practical experimental tools for the basic research on viral pathogenesis and applied research aimed at antiviral intervention for hemorrhagic ...
Ting Yao, Hang Liu, Yanfeng Yao, Wei Deng, Jiawen Sun, Zhenyu Kang, Ashaq Ali, Chao Shan, Zhiming Yuan, Fei Deng, Hualin Wang, Yun‐Jia Ning   +11 more
wiley   +1 more source

An Adolescent with Hyperimmunoglobulinemia D and Periodic Fever Syndrome Responding to Simvastatin Treatment

, 2011
The hyperimmunoglobulinemia D and periodic fever syndrome is proposed to be caused by a defect in the activity of mevalonate kinase enzyme which is involved in cholesterol and non-sterol isoprenoid biosynthesis.
BARIŞ, SAFA, Barlan, Isil B., Keles, Sevgi, ÖZDEMİR, Cevdet, Bahceciler, Nerin N., Karakoc-Aydiner, Elif   +5 more
core   +2 more sources