Results 111 to 120 of about 9,936 (203)

Altered Response of Progeria Fibroblasts to Epidermal Growth Factor

, 1991
peer reviewedThe Hutchinson-Gilford syndrome (progeria) is a rare disorder in childhood characterized by premature and accelerated aging. This study reports the effect of a potent growth factor, EGF, on the proliferative capacities and extracellular ...
Lapiere, ChM, Nusgens, Betty, Colige, Alain   +2 more
core  

Author Correction: Progerinin, an optimized progerin-lamin A binding inhibitor, ameliorates premature senescence phenotypes of Hutchinson-Gilford progeria syndrome. [PDF]

Commun Biol
Kang SM, Yoon MH, Ahn J, Kim JE, Kim SY, Kang SY, Joo J, Park S, Cho JH, Woo TG, Oh AY, Chung KJ, An SY, Hwang TS, Lee SY, Kim JS, Ha NC, Song GY, Park BJ.   +18 more
europepmc   +1 more source

Clinical imaging findings in a girl with Hutchinson-Gilford progeria syndrome

, 2012
[[abstract]]"Clinical imaging findings in a girl with Hutchinson-Gilford progeria syndrome: We report an 8½-year-old girl with premature aging, a karyotype of 46,XX and a de novo c.1824C>T mutation encoding p.G608G in the lamin A gene.
陳持平;Chen, Chih-Ping
core  

Extracellular matrix abnormalities in Hutchinson-Gilford progeria fibroblasts: a specific defect in collagen IV and basement membrane architecture? [PDF]

Matrix Biol Plus
Karmacharya S, Pasanen-Zentz AL, Busse F, Kronenberg NM, Chavez DRA, Al-Gburi S, Lerbs T, Brachvogel B, Velmans C, Tantcheva-Poor I, Wagener R, Paulsson M, Niessen CM, Gather MC, Krieg T, Schiavinato A.   +15 more
europepmc   +1 more source

Artificial intelligence-assisted reinterpretation of preclinical progeria research suggests a hierarchical nuclear-vascular resilience framework with translational implications. [PDF]

Int J Biol Sci
Madeddu P, Cattaneo M, Puca AA.
europepmc   +1 more source

A toxic STING-SAMHD1 axis drives replication stress in progeria and cancer cells. [PDF]

Nucleic Acids Res
Teodoro-Castro B, de Faria RC, Shashkova EV, Malique A, Adolph MB, Silva LND, Gonzalo S.   +6 more
europepmc   +1 more source

Epidural hematoma in a pediatric patient with Hutchinson-Gilford progeria syndrome: management considerations: a case report. [PDF]

Chin Neurosurg J
Ozmarasali AI, Sivas ZZ, Uguz I, Oto A.
europepmc   +1 more source

General anesthesia in patient with Hutchinson-Gilford Progeria syndrome: two case reports of dental treatment in the one patient. [PDF]

BMC Anesthesiol
Mankovsky B, Halushko O, Zablotskyy Y, Synytsyn M.   +3 more
europepmc   +1 more source

Progeria and hearing loss: parallels and divergences with presbycusis

openLa progeria, patologia rara caratterizzata da invecchiamento precoce, è un settore di ricerca ancora in evoluzione. Il primo gruppo di ricerca strutturato vede la luce solo all’inizio del secolo con la Progeria Research Foundation (PRF). L’obiettivo
VANGELISTA, GIORGIA
core  

LAV-BPIFB4 reverses progeria-associated cardiac aging by restoring diastolic function and reducing senescence. [PDF]

Int J Biol Sci
Chae U, Park YH, Kwon T, Chung KS, Kim SU.   +4 more
europepmc   +1 more source