Transmissible spongiform encephalopathy in the gray tremor mutant mouse.
, 1985 Gray tremor (gt) is an autosomal recessive mutation in the mouse linked to caracul (Ca) on chromosome 15. The complex mutant phenotype includes pigmentation defects, tremor, seizures, hypo- and dysmyelination in central and peripheral nervous systems,
Sidman, R L, Kinney, H C, Sweet, H O
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Spongiform Encephalopathy Following Allogeneic Cord Blood Transplant
, 2008 A 6 year old boy developed a fatal, rapidly progressive encephalopathy 5 months after a matched unrelated cord blood transplant. Autopsy findings revealed spongiform changes in his brain.
O\u27Brien, Dennis +4 more
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Quaking-induced conversion of prion protein on a thermal mixer accelerates detection in brains infected with transmissible spongiform encephalopathy agents. [PDF]
PLoS One, 2019 Kaelber N, Bett C, Asher DM, Gregori L.
europepmc +1 more source
, 2011 Transmissible spongiform encephalopathies (TSE), also known as prion diseases, are fatal neurodegenerative disorders present both in human and animals with different aetiology as they can occur genetically, spontaneously or by infection (Prusiner 1998 ...
Marzo, Ludovica
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Characterization of the prion protein in relation to normal cellular function and in disease [PDF]
, 2012 Transmissible spongiform encephalopathies (TSEs), also known as prion diseases, are a group of rare and fatal neurodegenerative disorders that can affect both human and animals.
Wik, Lotta
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Cross-seeding of prions by aggregated α-synuclein leads to transmissible spongiform encephalopathy. [PDF]
PLoS Pathog, 2017 Katorcha E +6 more
europepmc +1 more source
Transmissible Spongiform Encephalopathies of Animals
, 2016 Transmissible spongiform encephalopathies (TSEs) are neurodegenerative diseases caused by prions. Although these infections usually remain asymptomatic for years, the disease is always progressive and fatal once the clinical signs develop. TSEs affecting
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Assessing transmissible spongiform encephalopathy species barriers with an in vitro prion protein conversion assay. [PDF]
J Vis Exp, 2015 Johnson CJ +4 more
europepmc +1 more source
The glycosylation status of PrPC is a key factor in determining transmissible spongiform encephalopathy transmission between species. [PDF]
J Virol, 2015 Wiseman FK +8 more
europepmc +1 more source
Report of the Working Group `Overall Blood Supply Strategy with Regard to Variant Creutzfeldt-Jakob Disease (vCJD)' [PDF]
, 2009 von Koenig, Carl-Heinz Wirsing +19 more
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