Results 101 to 110 of about 12,655 (217)

An adult case of atypical hemolytic uremic syndrome presented with posterior reversible encephalopathy syndrome: Successful response to late-onset eculizumab treatment

Hematology Reports, 2018
Atypical hemolytic uremic syndrome is a rare and progressive disease caused by uncontrolled alternative complement activation. Dysregulatıon of the complement activation results in thrombotic microangiopathy and multiorgan damage.
Serife Solmaz Medeni, Sinem Namdaroglu, Tugba Cetintepe, Can Ozlu, Funda Tasli, Zehra Hilal Adibelli, Oktay Bilgir, Erhan Tatar   +7 more
doaj   +1 more source

FHR-1 binds to C-reactive protein and enhances rather than inhibits complement activation [PDF]

, 2017
Factor H (FH)-related protein 1 (FHR-1) is one of the five human factor H-related proteins, which share sequence and structural homology with the alternative pathway complement inhibitor FH.
Bánlaki, Zsófia, Cserhalmi, Marcell, Csincsi, Ádám, Józsi, Mihály, Kárpáti, Éva, Prohászka, Zoltán, Szabó, Z., Uzonyi, Barbara   +7 more
core   +1 more source

Actualización en síndrome hemolítico urémico atípico: diagnóstico y tratamiento. Documento de consenso [PDF]

, 2016
Trobareu una actualització (2015) d'aquest document a: http://hdl.handle.net/2445/99427Haemolytic uraemic syndrome (HUS) is a clinical entity defined as the triad of nonimmune haemolytic anaemia, thrombocytopenia, and acute renal failure, in which the ...
Arias, Manuel, Ariceta, Gema, Blasco, Miguel, Campistol Plana, Josep M., Espinosa, Mario, Grinyó Boira, Josep M., Praga, Manuel, Rodríguez de Córdoba, Santiago, Torra, Roser, Vilalta, Ramon (Vilalta Casas)   +9 more
core   +1 more source

Postoperative atypical hemolytic uremic syndrome in nontransplant setting: A case report with review of literature

Global Journal of Transfusion Medicine, 2018
Atypical hemolytic uremic syndrome (aHUS) is a clinical diagnosis characterized by a triad of microangiopathic hemolytic anemia, thrombocytopenia, and renal dysfunction. Postoperative aHUS in nontransplant patients is a rare entity.
Anil Khetarpal, Vidhi Gupta, Urvershi Kotwal   +2 more
doaj   +1 more source

Atypical hemolytic-uremic syndrome, manifesting without thrombocytopenia (clinical case)

Известия высших учебных заведений. Поволжский регион: Медицинские науки
Background. Atypical hemolytic uremic syndrome is an ultra-rare (orphan) disease from the group of thrombotic microangiopathies of progressive course, which is caused by uncontrolled activation of the alternative complement pathway of hereditary or ...
A.A. Dyachkova, A.N. Anokhin, M.A. Shlykova, I.S. Kiseleva   +3 more
doaj   +1 more source

Concurrent Atypical Hemolytic Uremic Syndrome and Autoimmune Hemolytic Anemia: a case report

Caspian Journal of Pediatrics, 2018
Background: Atypical hemolytic uremic syndrome (aHUS) is a life-threatening and scarce disorder characterized by acute renal failure and disease, non-immune microangiopathic hemolytic anemia and thrombocytopenia, leading to end-stage renal failure or ...
Sayed Yousef Mojtahedi, Mohammad Kaji Yazdi   +1 more
doaj  

Plasma resistant atypical hemolytic uremic syndrome associated with a CFH mutation treated with eculizumab: a case report [PDF]

, 2015
INTRODUCTION: Thrombotic microangiopathies are a group of diseases presenting as microangiopathic hemolytic anemia, thrombocytopenia and end-organ dysfunction.
Abdulkadir Unsal, Cuneyt Akgol, David Kavanagh, Ekrem Kara, Elbis Ahbap, Mustafa Sevinc, Tamer Sakaci, Taner Basturk, Tim HJ Goodship, Tuncay Sahutoglu, Vicky Brocklebank, Yener Koc   +11 more
core   +1 more source

Managing atypical hemolytic uremic syndrome: chapter 2 [PDF]

Kidney International, 2015
Licht et al. present the 2-year follow-up data of the landmark trials studying the efficacy of eculizumab in the treatment of atypical hemolytic uremic syndrome (aHUS). They report sustained improvements in hematologic parameters, continued safety, and additional improvements in kidney function with extended treatment.
openaire   +2 more sources

Administração profiláctica de plasma no síndrome hemolítico urémico atípico recorrente [PDF]

, 2006
O síndrome hemolítico urémico (SHU) define- se pela ocorrência simultânea de anemia hemolítica microangiopática, trombocitopenia e insuficiência renal aguda.
Almeida, Marta Pinto de, Barbot, José, Costa, Elísio, Costa, Elísio, Costa, Teresa, Faria, Maria Sameiro, Mota, Conceição, Pereira, Elói   +7 more
core  

Clinical practice guidelines for the management of atypical haemolytic uraemic syndrome in the United Kingdom [PDF]

, 2010
,, Goodship, Tim H J, Machin, Sam, Taylor, C Mark, Wigmore, Stephen J   +4 more
core   +1 more source