Results 21 to 30 of about 3,095,271 (376)
HAE-AS, a specific disease activity scale for hereditary angioedema with C1-inhibitor deficiency.
Journal of investigational allergology & clinical immunology, 2020 BACKGROUND AND OBJECTIVE Hereditary angioedema due to C1-inhibitor deficiency (C1-INH-HAE) shows variability in disease activity among patients and within individual patients.
M. JoãoForjaz +5 more
semanticscholar +1 more source
Медицинская иммунология, 2023 C1 inhibitor of serine proteases (C1-INH) performs a regulatory function in the complement system and vascular permeability. Deficiency of C1-INH leads to various forms of angioedema, including hereditary angioedema (HAE).
N. P. Gorbunov +12 more
doaj +1 more source
Hereditary angioedema (HAE) in children and adolescents : a consensus on therapeutic strategies [PDF]
, 2012 Hereditary angioedema due to C1 inhibitor (C1 esterase inhibitor) deficiency (types I and II HAE-C1-INH) is a rare disease that usually presents during childhood or adolescence with intermittent episodes of potentially life-threatening angioedema ...
Aberer, Werner +11 more
core +1 more source
Deciphering the Genetics of Primary Angioedema with Normal Levels of C1 Inhibitor
Journal of Clinical Medicine, 2020 The genetic alteration underlying the great majority of primary angioedema with normal C1 inhibitor (nl-C1-INH-HAE) cases remains unknown. To search for variants associated with nl-C1-INH-HAE, we genotyped 133 unrelated nl-C1-INH-HAE patients using a ...
Gedeon Loules +16 more
semanticscholar +1 more source
Spectrum of diagnosis of hereditary angioedema: Seven case reports
Indian Journal of Allergy Asthma and Immunology, 2020 Hereditary angioedema (HAE) is a potentially life-threatening disorder, due to a mutation in complement one-inhibitor (C1-INH) gene, which blocks the activity of various components of complement – fibrinolytic and bradykinin control system.
P C Kathuria +2 more
doaj +1 more source
Study on separation and purification process of C1 esterase inhibitor
Zhongguo shuxue zazhi, 2022 Objective To study the technology of separating and purifying C1 esterase inhibitor (C1-INH) by using the waste washing liquid as raw materia during the preparation of human prothrombin complex (PCC) l.
Jiabin XU +4 more
doaj +1 more source
Activation of coagulation factor XI, without detectable contact activation in dengue haemorrhagic fever [PDF]
, 2001 A prospective cohort study was performed in 50 patients with dengue haemorrhagic fever (DHF) to determine the potential role of the contact activation system and factor XI activation (intrinsic pathway) in the coagulation disorders in DHF.
Bajzar +29 more
core +2 more sources
Frontiers in Cellular Neuroscience, 2014 Traumatic brain injury (TBI) induces a strong inflammatory response which includes blood-brain barrier damage, edema formation and infiltration of different immune cell subsets.
Christiane eAlbert-Weissenberger +12 more
doaj +1 more source
Optimum Use of Acute Treatments for Hereditary Angioedema: Evidence-Based Expert Consensus
Frontiers in Medicine, 2018 Acute treatment of hereditary angioedema due to C1 inhibitor deficiency has become available in the last 10 years and has greatly improved patients’ quality of life.
Hilary Longhurst
doaj +1 more source
Hereditary angioedema: Diagnostic algorithm and current treatment concepts
Indian Dermatology Online Journal, 2021 Hereditary angioedema (HAE) is an uncommon disorder with a global prevalence of approximately 1 in 10,000 to 1 in 50,000 population. This disease is grossly underrecognized in India because of lack of awareness and/or lack of diagnostic facilities ...
Ankur Kumar Jindal +2 more
doaj +1 more source