Results 11 to 20 of about 878,820 (240)

Treatment of hereditary angioedema with plasma-derived C1 inhibitor

Therapeutics and Clinical Risk Management, 2008
Michael J Prematta, Tracy Prematta, Timothy J CraigSection of Allergy and Immunology, Penn State University, Milton S. Hershey Medical Center, PA, USABackground: Plasma-derived C1 inhibitor (C1-INH) concentrate is a treatment option for acute hereditary ...
Michael J Prematta, Tracy Prematta, Timothy J Craig   +2 more
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Lymphoproliferative disease and acquired C1 inhibitor deficiency

Haematologica, 2007
Angioedema due to acquired deficiency of the C1-inhibitor is a bridging condition between autoimmunity and lymphoproliferation. We report 32 patients with acquired C1 inhibitor deficiency: 23 have anti C1-inhibitor autoantibodies; 13 have monoclonal ...
Roberto Castelli, Daniela Lambertenghi Deliliers, Lorenza C. Zingale, Enrico Maria Pogliani, Marco Cicardi   +4 more
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Monocyte C1-Inhibitor Synthesis [PDF]

, 1987
C1-inhibitor is the major control protein of the classical pathway of complement. In man, its hereditary deficiency results in the clinical condition of hereditary angio-oedema (HAE).
Jones, Linda Margaret
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Hereditary angioedema (HAE) in children and adolescents : a consensus on therapeutic strategies [PDF]

, 2012
Hereditary angioedema due to C1 inhibitor (C1 esterase inhibitor) deficiency (types I and II HAE-C1-INH) is a rare disease that usually presents during childhood or adolescence with intermittent episodes of potentially life-threatening angioedema ...
Martinez-Saguer, I, Wahn, V, V. Wahn, I. Martinez-Saguer, Magerl, Markus, Eberl, W, Meyer-Olson, D, Kurnik, K, P. Staubach-Renz, Staubach-Renz, Petra, Eberl, Wolfgang, Kreuz, Wolfhart, Faßhauer, M, K. Kurnik, Magerl, M, D. Meyer-Olson, T. Kühne, W. Aberer, Staubach-Renz, P, Späth, Peter J., Aberer, W, Späth, P, Kreuz, W, Kurnik, Karin, W. Eberl, Wahn, Volker, P. Späth, Aberer, Werner, Meyer-Olson, Dirk, Martinez Saguer, Inmaculada, M. Faßhauer, W. Kreuz, Faßhauer, Maria, M. Magerl, Kühne, T, Kühne, Thomas   +35 more
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Effects of weak anchoring on C1 and C2 chevron structures [PDF]

, 2005
We present a theoretical study of the effect of weak anchoring on the transition between C1 and C2 chevron structures in smectic C liquid crystals. We employ a continuum theory which allows for variable cone, azimuthal and layer tilt angles.
Mottram, Nigel, McKay, Geoffrey, Diaz, A.   +2 more
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Study on separation and purification process of C1 esterase inhibitor

Zhongguo shuxue zazhi, 2022
Objective To study the technology of separating and purifying C1 esterase inhibitor (C1-INH) by using the waste washing liquid as raw materia during the preparation of human prothrombin complex (PCC) l.
Jiabin XU, Yawen LI, Jiali GONG, Erhua LUO, Meng ZHANG   +4 more
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HAE international home therapy consensus document [PDF]

, 2010
Hereditary angioedema (C1 inhibitor deficiency, HAE) is associated with intermittent swellings which are disabling and may be fatal. Effective treatments are available and these are most useful when given early in the course of the swelling.
Bowen, Tom, Craig, Timothy, Boysen, Henrik, E. Aygören Pürsün, Janet Long, Zuraw Bruce, Avner Reshef, Longhurst, Hilary J., Cicardi Marco, Bygum, Anette, Hilary J Longhurst, Bruce Zuraw, Anette Bygum, Martinez-Saguer, Inmaculada, Bork Konrad, Inmaculada Martinez-Saguer, Sofia Grigoriadou, Caballero, Teresa, Claire Bethune, I. Martinez Saguer, Reshef Avner, Martinez Saguer, Inmaculada, M. Raguet, H. J. Longhurst, J. Bjorkander, Laurence Bouillet, Levi Marcel M, Raguet Michel, Timothy Craig, Bethune Claire, T. Bowen, Michel Raguet, L. Bouillet, Marco Cicardi, Gompels Mark, Bork, Konrad, C. Bethune, Dempster, John, Huffer Ursula, Marcel M Levi, Longhurst, Hilary, Aygören-Pürsün Emel, M. Cicardi, Farkas Henriette, Henriette Farkas, Raguet, Michel, Bygum Anette, Bjorkander Janne, Levi, Marcel M, Longhurst Hilary J, Martinez-Saguer Inmaculada, Teresa Caballero, Ursula Huffer, Bouillet, Laurence, H. Farkas, Boysen Henrik, Huffer, Ursula, M. M. Levi, M. Gompels, Gompels, Mark, S. Grigoriadou, Kreuz, Wolfhart, Janne Bjorkander, A. Bygum, Craig Timothy, Longhurst, Hilary J, Farkas, Henriette, Bygum, Anette; id_orcid, Bowen Tom, Gooi Jimmy, Bouillet Laurence, Boysen, Henrik B., A. Reshef, J. Gooi, J. Dempster, Konrad Bork, Henrik Boysen, Gooi, Jimmy, Jimmy Gooi, Cicardi, Marco, T. Craig, B. Zuraw, Caballero Teresa, Bethune, Claire, U. Huffer, Levi, Marcel M., Dempster John, John Dempster, Grigoriadou Sofia, Reshef, Avner, Long Janet, H. Boysen, Grigoriadou, Sofia, Bjorkander, Janne, T. Caballero, Tom Bowen, Zuraw, Bruce, J. Long, W. Kreuz, Mark Gompels, Emel Aygören-Pürsün, Aygören-Pürsün, Emel, K. Bork, Kreuz Wolfhart, Long, Janet, Wolfhart Kreuz   +105 more
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C1-Inhibitor protects from focal brain trauma in a cortical cryolesion mice model by reducing thrombo-inflammation

Frontiers in Cellular Neuroscience, 2014
Traumatic brain injury (TBI) induces a strong inflammatory response which includes blood-brain barrier damage, edema formation and infiltration of different immune cell subsets.
Christiane eAlbert-Weissenberger, Stine eMencl, Michael K. Schuhmann, Irmak eSalur, Eva eGöb, Friederike eLangenhauser, Sarah eHopp, Nelli eHennig, Sven G Meuth, Sven G Meuth, Marc W. Nolte, Anna-Leena eSirén, Christoph eKleinschnitz   +12 more
doaj   +1 more source

Risk of angioedema following invasive or surgical procedures in HAE type I and II : the natural history [PDF]

, 2013
Background: Hereditary angioedema (HAE), caused by deficiency in C1-inhibitor (C1-INH), leads to unpredictable edema of subcutaneous tissues with potentially fatal complications.
Aygören-Pürsün, Emel, Kreuz, Wolfhart, Martinez Saguer, Inmaculada, Klingebiel, Thomas, Schwabe, Dirk   +4 more
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2010 international consensus algorithm for the diagnosis, therapy and management of hereditary angioedema [PDF]

, 2010
Background We published the Canadian 2003 International Consensus Algorithm for the Diagnosis, Therapy, and Management of Hereditary Angioedema (HAE; C1 inhibitor [C1-INH] deficiency) and updated this as Hereditary angioedema: a current state-of-the-art ...
S. Waserman, Harmat, George, E. Leith, Bernstein Jonathan, Bowen, Tom, Leith, Eric, Doris Neurath, Craig, Timothy, Paul K Keith, Eric Leith, A. Hamed, D. Moldovan, Zuraw Bruce, Betschel Stephen, Avner Reshef, Dean, John, Cicardi Marco, Moldovan, Dumitru, Lilian Varga, Hilary J Longhurst, Rowe Anne, Nordenfelt Patrik, Barbara Mako, Harmat George, B. Ritchie, Martinez-Saguer, Inmaculada, Fust George, Della Cogar, Inmaculada Martinez-Saguer, George Fust, Devaraj, Ramachand, Mike Frank, Richard Warrington, J. Bernstein, Rowan, Dereth, Nielsen Erik W, Li, Henry, Tsai Ellie, D. Cogar, Timothy Craig, Zhi Xiang, Poon Man-Chiu, J. Brosz, E. Tsai, Marco Cicardi, R. Schellenberg, R. Warrington, Sur, Smeeksha, B. Mako, I. Nagy, Bork, Konrad, Frank Mike, George Harmat, Frank, Mike, Karen Binkley, H. Lyons, Schellenberg, Robert, Longhurst, Hilary, Erik W Nielsen, L. Varga, Farkas Henriette, Henriette Farkas, Mako, Barbara, Devaraj Ramachand, Longhurst Hilary J, G. E. Rivard, Rusicke, Eva, Hamed, Azza, Kreuz, Wolfhart, Eva Rusicke, Poon, Man-Chiu, Späth, Peter, Binkley Karen, Anne Rowe, Craig Timothy, Istvan Nagy, Neurath, Doris, Xiang, Zhi Yu, Bowen Tom, E. W. Nielsen, Lacuesta, Gina, Sean Mace, Bouillet Laurence, Nagy Istvan, Lacuesta Gina, Brosz Kristylea, Nielsen, Erik W, John Brosz, D. Rowan, D. Neurath, Peter Späth, A. Kanani, Nagy, Istvan, Ameratunga Rohan, Bruce Ritchie, Aygoeren-Pürsün Emel, Li Henry, A. Rowe, G. Lacuesta, Keith Paul K, B. Zuraw, T. Craig, Ritchie, Bruce, Caballero Teresa, Cogar Della, S. Mace, M. Frank, Dumitru Moldovan, S. Betsche, Mace Sean, M. Poon, Zhi Yu Xiang, Lyons, Harriet, Waserman Susan, J. Dean, T. Caballero, Xiang Zhi, Tom Bowen, Rohan Ameratunga, Gina Lacuesta, M. Levi, Smith-Foltz Sarah, S. Sur, Brosz, John, Björkander, Janne, Aygören-Pürsün, Emel, Warrington Richard, Aygoeren-Pürsün, Emel, Susan Waserman, Binkley, Karen, Waserman, Susan, Ritchie Bruce, Donald Stark, Keith, Paul K, Xiang, Zhi Y, Bygum, Anette, Bruce Zuraw, Anette Bygum, H. Li, R. Ameratunga, Bork Konrad, Robert Schellenberg, Rivard Georges-Etienne, Sarah Smith-Foltz, Caballero, Teresa, I. Martinez Saguer, Reshef Avner, Martinez Saguer, Inmaculada, H. J. Longhurst, Varga Lilian, J. Björkander, Laurence Bouillet, Palinder Kamra, Leith Eric, Betschel, Stephen, Bernstein, Jonathan, Ellie Tsai, T. Bowen, K. Brosz, Ramachand Devaraj, J. Hebert, Rowe, Anne, L. Bouillet, Kristylea Brosz, Dereth Rowan, Marcel Levi, Neurath Doris, P. Späth, Kanani, Amin, G. Harmat, M. Cicardi, Kanani Amin, Bygum Anette, Stephen Betschel, Sur Smeeksha, Martinez-Saguer Inmaculada, G. Fust, Nordenfelt, Patrik, Teresa Caballero, Bouillet, Laurence, Fust, George, H. Farkas, Jonathan Bernstein, Levi, Marcel, Jacques Hebert, Keith, Paul K., Stark, Donald, P. Nordenfelt, Hebert, Jacques, Xiang, Zhi, Warrington, Richard, D. Stark, Harriet Lyons, A. Bygum, Longhurst, Hilary J, Stark Donald, Henry Li, Rowan Dereth, Farkas, Henriette, Lyons Harriet, Bygum, Anette; id_orcid, Levi Marcel, Kamra, Palinder, Dean John, Ameratunga, Rohan, E. Aygoeren Pürsün, A. Reshef, Brosz, Kristylea, Janne Björkander, R. Devaraj, Konrad Bork, P. K. Keith, Björkander Janne, Kamra Palinder, Bernstein, Jonathan A., Späth Peter, Azza Hamed, Schellenberg Robert, P. Kamra, Cicardi, Marco, Amin Kanani, Mace, Sean, Smeeksha Sur, Levi, Marcel M., Y. X. Zhi, Varga, Lilian, Reshef, Avner, S. Smith Foltz, Georges-Etienne Rivard, Rusicke Eva, Rivard, Georges-Etienne, Smith-Foltz, Sarah, K. Binkley, Yu Xiang, Zhi, Emel Aygoeren-Pürsün, Cogar, Della, Hebert Jacques, Patrik Nordenfelt, E. Rusicke, Brosz John, John Dean, Mako Barbara, Zuraw, Bruce, Moldovan Dumitru, W. Kreuz, K. Bork, Tsai, Ellie, Kreuz Wolfhart, Man-Chiu Poon, Wolfhart Kreuz, Nielsen, Erik W., Hamed Azza   +251 more
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