Frontiers in Immunology, 2018 Because of the morbidity and limited therapeutic options of autoimmune diseases, there is a high, and thus far, unmet medical need for development of novel treatments.
Unni K. Samavedam +22 more
doaj +1 more source
Inflammatory epidermolysis bullosa acquisita with coexistent IgA antibodies to plectin
, 2005 We present a case of inflammatory epidermolysis bullosa acquisita (EBA) with IgA antibodies to plectin. Analysis of lesional skin biopsies by electron microscopy revealed the split level to be in the sublamina densa zone, corresponding to the diagnosis ...
Buijsrogge, JJA +5 more
core +1 more source
A case report of the use of rituximab and the Epidermolysis Bullosa Disease Activity Scoring Index (EBDASI) in a patient with epidermolysis bullosa acquisita with extensive esophageal involvement [PDF]
, 2018 A 49-year-old man with recalcitrant mechanobullous epidermolysis bullosa acquisita (EBA) with significant esophageal involvement was treated with rituximab. EBA is a chronic autoimmune subepidermal bullous disease.
Yang, Anes +3 more
core +1 more source
Pyoderma Gangrenosum as the First Manifestation of Inflammatory Bowel Disease: A Case Report
Case Reports in Gastrointestinal Medicine, Volume 2026, Issue 1, 2026.Approximately 50% of patients with inflammatory bowel disease (IBD) exhibit extraintestinal manifestations, among which skin and mucosal lesions are common. However, pyoderma gangrenosum occurs in only 1%‐2% of IBD patients. We report the case of a 23‐year‐old male patient who was admitted to the hospital with pyoderma gangrenosum that was unresponsive
Nam Hoai Nguyen +7 more
wiley +1 more source
, 1997 Epidermolysis bullosa acquisita (EBA) is rarely reported in childhood, but we now describe a 6-year-old Korean girl with the condition. She presented with multiple tense bullae annularly distributed on the perioral, periorbital and genital areas, and was
김수찬
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Spontaneous autoimmune subepidermal blistering diseases in animals: a comprehensive review
BMC Veterinary Research, 2023 Autoimmune subepidermal blistering diseases (AISBDs) are rare skin disorders of animals that were first identified in dogs but several AISBDs are now recognised in other companion animal species.
Petra Bizikova +3 more
doaj +1 more source
Use of Janus Kinase Inhibitors in the Treatment of Genodermatoses: A Systematic Review
Dermatologic Therapy, Volume 2026, Issue 1, 2026.Introduction Genodermatoses are rare inherited skin disorders with limited treatment options. Emerging evidence suggests Janus kinase (JAK) inhibitors may offer therapeutic benefits by modulating underlying immune and inflammatory pathways. This study aims to systematically review the efficacy and safety of JAK inhibitors in treating genodermatoses ...
Pin-Chun Chen +4 more
wiley +1 more source
Fatal vascular involvement in systemic lupus erythematosus following epidermolysis bullosa acquisita
, 1995 Epidermolysis bullosa acquisita may be associated with various systemic diseases, including systemic lupus erythematosus. We describe the clinical and immunological findings in a 38-year-old women with epidermolysis bullosa acquisita and systemic lupus ...
이광훈
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Functional Heterogeneity of Immune Complexes in Epidermolysis Bullosa Acquisita [PDF]
, 1987 Epidermolysis bullosa acquisita is an inflammatory subepidermal bullous disease characterized by circulating and tissue-bound complement-binding anti-basement membrane zone autoantibodies to type VII procollagen.
Briggaman, Robert A. +3 more
core +1 more source
Reduced Skin Blistering in Experimental Epidermolysis Bullosa Acquisita After Anti-TNF Treatment
Molecular Medicine, 2016 Epidermolysis bullosa acquisita (EBA) is a difficult-to-treat subepidermal autoimmune blistering skin disease (AIBD) with circulating and tissue-bound anti-type VII collagen antibodies.
Misa Hirose +13 more
doaj +1 more source