Results 41 to 50 of about 28,196 (246)

Liver Transplantation for Alagille's Syndrome [PDF]

, 1993
Twenty-three children with Alagille's syndrome and end-stage liver disease underwent liver transplantation with cyclosporine and low-dose steroid immunosuppression. Two to 9 years (mean, 4.4 years) after surgery, 13 (57%) of the children were still alive,
Reyes, J, Starzl, TE, Tepetes, K, Todo, S, Tzakis, AG, Tzoracoleftherakis, V   +5 more
core   +1 more source

Benign Recurrent Intrahepatic Cholestases [PDF]

, 2001
Benign recurrent intrahepatic cholestasis (BRIC) or idiopathic recurrent intrahepatic cholestasis is a rare case. It is a familial and autosomal recessive. The etiology of BRIC is still unknown. We report the case of a patient with BRIC who suffered from
Akbar, F. N. (Femmy), Budihusodo, U. (Unggul), Lesmana, L. A. (L), Marwoto, W. (Wirasmi), Noer, S. (Sjaifoellah)   +4 more
core   +1 more source

Coexisting Sickle Cell Anemia and Sarcoidosis: A Management Conundrum! [PDF]

, 2017
Sickle cell disease and Sarcoidosis are conditions that are more common in the African American population. In this report we share an unfortunate patient who had hepatic sarcoidosis but could not receive steroids since that precipitated acute liver ...
Gollahalli, Nagesh S., Nutan, FNU
core   +3 more sources

DIFFERENCES OF BIRTH WEIGHT AND ONSET OF ACHOLIC STOOL BETWEEN EXTRAHEPATIC AND INTRAHEPATIC CHOLESTASIS

Indonesian Midwifery and Health Sciences Journal
Background: Biliary atresia (extrahepatic cholestasis) and neonatal hepatitis (intrahepatic cholestasis) are two main causes of cholestasis. It is important to distinguish the type of cholestasis for determine management.
Bagus Setyoboedi, Lasmauli Situmorang, Rendi Aji Prihaningtyas, Sjamsul Arief   +3 more
doaj   +1 more source

Benign recurrent intrahepatic cholestasis (BRIC): Evidence of genetic heterogeneity and delimitation of the BRIC locus to a 7-cM interval between D18S69 and D18S64 [PDF]

, 1997
Benign recurrent intrahepatic cholestasis (BRIC) is an autosomal recessive liver disease characterized by multiple episodes of cholestasis without progression to chronic liver disease.
Amstel, H.K.P. van, Berge Henegouwen, G.P. (Gerard) van, Berger, R. (Ruud), Bijleveld, C.M.A. (Charles M.), Bull, I.D. (Ian), Carlton, V.E.H. (Victoria E.), Delhaas, T. (Tammo), Freimer, N.B. (Nelson), Hattum, J. (Jan) van, Houwen, R.H.J. (Roderick), Juijn, J.A. (Jenneke), Keller, K.M. (Klaus), Knol, I.E. (Irma), Pearson, P.L., Sinaasappel, M. (Maarten), Sinke, R.J. (Richard)   +15 more
core   +4 more sources

Assessment of aspartate aminotransferase to Platelet Ratio Index and Fibrosis-4 Index score on women with intrahepatic cholestasis of pregnancyAJOG Global Reports at a Glance

AJOG Global Reports
BACKGROUND: Intrahepatic cholestasis of pregnancy is a pregnancy-related liver condition that is characterized by elevated liver function tests and/or bile acids in the presence of pruritis.
Maria Cemortan, PhD, Corina Iliadi-Tulbure, PhD, Irina Sagaidac, PhD, Olga Cernetchi, PhD   +3 more
doaj   +1 more source

Generation of a bile salt export pump deficiency model using patient-specific induced pluripotent stem cell-derived hepatocyte-like cells [PDF]

, 2017
Bile salt export pump (BSEP) plays an important role in hepatic secretion of bile acids and its deficiency results in severe cholestasis and liver failure.
Harada Kazuo, Hirata Kazumasa, Imagawa Kazuo, Isoyama Shigemi, Kage Masayoshi, Kawabata Kenji, Mizuguchi Hiroyuki, Noguchi Emiko, Sakurai Fuminori, Shinkai Masato, Sumazaki Ryo, Tachibana Masashi, Takayama Kazuo, Tanikawa Ken, 今川 和生, 野口 惠美子   +15 more
core   +1 more source

The debut of benign recurrent intrahepatic cholestasis in acute hepatitis A

Трансплантология (Москва)
Background. Benign recurrent intrahepatic cholestasis is a rare inherited disorder characterized by recurrent episodes of severe hyperbilirubinemia and pruritus that resolve spontaneously.
K. Yu. Kokina, Yu. O. Malinovskaya, O. V. Sumtsova, A. O. Grigorevskaya, Ya. G. Moysyuk   +4 more
doaj   +1 more source

An Insight Into Neonatal Cholestasis; A Tertiary Care Hospital Experience in Rawalpindi, Pakistan

Pakistan Armed Forces Medical Journal, 2023
Objective: To determine the frequencies of various etiologies of neonatal cholestasis diagnosed by clinical findings and laboratory investigations at the Pak Emirates Military Hospital, Rawalpindi, Pakistan.
Sughra Azhar, Farooq Ikam, Sarina Zainab Shirazi, Junaid Altaf, Rahmeen Pervaiz   +4 more
doaj   +1 more source

Recent advances in the exploration of the bile salt export pump (BSEP/ABCB11) function [PDF]

, 2016
ntroduction: The bile salt export pump (BSEP/ABCB11), residing in the apical membrane of hepatocyte, mediates the secretion of bile salts into the bile.
Homolya, László, Telbisz, Ágnes Mária   +1 more
core   +1 more source