Results 81 to 90 of about 6,446 (159)

Development and validation of a quality of life scale for pediatric mastocytosis

Allergy, Asthma & Clinical Immunology
Background Mastocytosis imposes a considerable burden on patients’ quality of life. While validated QoL instruments are available for adults with systemic mastocytosis, no disease-specific quality-of-life measure has yet been developed for pediatric ...
Aslı Berivan Topçak, Ece Tüsüz Önata, Şeyma Genç, Sefika Ilknur Kökcü Karadag, Nilay Çalışkan, Güler Yıldırım, Hamit Boloğur, Hilal Güngör, Merve Karaca Şahin, Muhammed Fatih Erbay, Hasan Tunç Şarman, Özlem Terzi, Emek Kocatürk, Frank Siebenhaar, Öner Özdemir, Deniz Özçeker   +15 more
doaj   +1 more source

Challenges in the Diagnosis of Cutaneous Mastocytosis

Diagnostics
Background: Mastocytosis is characterized by an accumulation of clonal mast cells (MCs) in tissues such as the skin. Skin lesions in mastocytosis may be clinically subtle or heterogeneous, and giving the correct diagnosis can be difficult.
Knut Brockow, Rebekka Karolin Bent, Simon Schneider, Sophie Spies, Katja Kranen, Benedikt Hindelang, Zsuzsanna Kurgyis, Sigurd Broesby-Olsen, Tilo Biedermann, Clive E. Grattan   +9 more
doaj   +1 more source

Pediatric Mastocytosis

Journal of Investigative Dermatology, 1991
The onset of mastocytosis occurs between birth and 2 years of age in approximately 55% of all cases; an additional 10% develop the disease before the age of 15 years. Mastocytosis in these age groups differs in many respects from mastocytosis that has its onset in adulthood. The typical presentation of pediatric-onset mastocytosis consists of cutaneous
Kettelhut, Brett V., Metcalfe, Dean D.
openaire   +4 more sources

Mastocytosis - diagnosis and classification

, 2009
Mastocytosis is a heterogeneous group of disorders with different severity and prognosis, which are characterized by excessively increased numbers of mast cells in the skin or in other tissues.
Brockow, K;Behrendt, H;Ring, J
core   +1 more source

Mastocytosis: One Word for Different Diseases

Oncology and Therapy, 2018
Mastocytosis is a neoplastic disease originating from tissue infiltration by transformed mast cells. The diagnosis requires a high grade of suspicion due to the large variety of presenting symptoms. The World Health Organization classification recognizes
Marianna Criscuolo, Luana Fianchi, Alessio M. E. Maraglino, Livio Pagano   +3 more
doaj   +1 more source

Cutaneous mastocytosis

, 2011
Background: Mastocytosis is a heterogeneous group of rare diseases characterized by the proliferation and accumulation of mast cells in body tissues. It usually presents in the skin, but may affect other tissues, especially the bone marrow, liver, spleen,
ENGİN, BURHAN, TÜZÜN, YALÇIN, Yardımcı, Gürkan, Kutlubay, Zekayi   +3 more
core  

Mastocytosis of the female breast

, 2010
A subset of patients with systemic mastocytosis may manifest with extracutaneous involvement. To the best of our knowledge, mastocytosis of the human breast has not been described. This study reports a case with mastocytosis involving the breasts of a 33-
Pantanowitz, Liron, MD, Setia, Namrata, MD, Crisi, Giovanna, MD   +2 more
core   +1 more source

Clinicopathological Features and Prognosis of Pediatric Mastocytosis: A 15-Year Experience with Emphasis on Disease Evolution

Clinical, Cosmetic and Investigational Dermatology
Qiannan Jia, Weiqi Wang, Shuaixin Li, Xinran Li, Aiping Fan, Dian Zheng, Siying Li, Jun LiDepartment of Dermatology, State Key Laboratory of Complex Severe and Rare Diseases, Peking Union Medical College Hospital, Chinese Academy of Medical Sciences and ...
Jia Q, Wang W, Li S, Li X, Fan A, Zheng D, Li S, Li J   +7 more
doaj  

Challenges in Cutaneous Mastocytosis

Cutaneous lesions of mastocytosis (CLM) are a hallmark for the diagnosis of mastocytosis. The nomenclature of the term "cutaneous mastocytosis" (CM) is ambiguous as it is used both for classification excluding and as a morphologic description including ...
Rupp, Svenja, Franz, Tobias;Hubbuch, Mara;Rupp, Svenja;Brockow, Knut, Brockow, Knut, Franz, Tobias, Hubbuch, Mara   +4 more
core   +1 more source

Diffuse large B cell lymphoma coexistence with systemic mastocytosis

Journal of Cancer Research and Practice, 2016
Systemic mastocytosis is a rare disease and characterized by excessive mast cell accumulation in one or multiple organs. One subtype of systemic mastocytosis is systemic mastocytosis-associated clonal hematological non-mast cell lineage disease (SM-AHMND)
Sheng-Hsuan Chien, Yao-Chung Liu, Ying-Chung Hong, Ching-Fen Yang, Chun-Yu Liu, Tzeon-Jye Chiou, Cheng-Hwai Tzeng, Jin-Hwang Liu, Jyh-Pyng Gau   +8 more
doaj   +1 more source