Results 141 to 150 of about 1,936,204 (283)

Biallelic PIGB Variants Cause Motor Neuropathy with Conduction Blocks and Peripheral Nerve Hyperexcitability

Annals of Neurology, EarlyView.
Objective Glycosylphosphatidylinositol (GPI)‐anchored proteins play critical roles in nervous system function. Pathogenic variants in genes involved in GPI‐anchor biosynthesis cause early‐onset multisystem disorders known as inherited GPI deficiencies. We describe a novel neuromuscular phenotype associated with PIGB deficiency.
Gorka Fernández‐Eulate, Romain Duval, Marina Konyukh, Alessandro Bertini, Ayse Candayan, Albena Jordanova, Theresa Brunet, Wolfgang Müller‐Felber, Helena F. Pernice, Katrin Hahn, Nadja Ehmke, Juliane Beuschlein, Bertrand Isidor, Benjamin Cogné, Yann Péréon, Annabelle Chaussenot, John Rendu, Aysylu Murtazina, Dmitrii Subbotin, Artem Borovikov, Andrey Marakhonov, Chiara Pisciotta, Paola Saveri, Daniele Cazzato, Lucie Lemeray, Bérengère Koehl, Jean‐Madeleine de Sainte‐Agathe, Stefano Facchini, Ilaria Quartesan, Andrea Cortese, Yesim Parman, Arman Cakar, Davide Pareyson, Slim Azouzi, Tanya Stojkovic   +34 more
wiley   +1 more source

Dark Heritage Prospection ‐ Mapping the Treblinka II Extermination Camp Using a Magnetometer Survey and Integrated Archival Sources

Archaeological Prospection, EarlyView.
ABSTRACT The history of Nazi German extermination camps has, until recently, relied primarily on eyewitness testimony. Very few official documents detailing the facilities survived the war due to the special operation ‘Sonderaktion 1005’, dedicated to hiding their existence and extent.
Sebastian Różycki, Michał Pisz, Paweł Bylina, James Walker, Lucy Benoit   +4 more
wiley   +1 more source

Ferritin as a Nanoparticle Scaffold for Plant‐Produced Next‐Generation Subunit Vaccines

Biotechnology and Bioengineering, EarlyView.
ABSTRACT Protein nanoparticles offer an innovative approach to next‐generation subunit vaccine development by displaying antigenic sequences on the nanoparticle surface. Compared to traditional subunit vaccines, protein nanoparticle vaccines often show improved interaction with the immune system due to their particulate size and repetitive epitope ...
Jordan T. VanderBurgt, Richard Strasser, Christopher P. Garnham, Rima Menassa   +3 more
wiley   +1 more source

Neurovascular coupling in bone regeneration: Mechanisms, advanced biomaterials and challenges

BMEMat, EarlyView.
This figure illustrates various material strategies for neurovascularized bone regeneration, including electroactive scaffolds, ion‐loaded materials, drug delivery systems, surface modifications, cells/cell products, growth factors, and peptides. These approaches aim to synergistically promote the regeneration of neural, vascular, and bone tissues ...
Yixin Ma, Nan Jiang, Liyuan Chen, He Zhang, Xinjia Cai, Karan Gulati, Danqing He, Zhigang Cai, Yan Liu   +8 more
wiley   +1 more source

Perovskite Photodetectors at the Intelligence Frontier: From Tunable Materials to Adaptive Optoelectronic Systems

Carbon Energy, EarlyView.
This comprehensive review presents a progressive roadmap for perovskite vision detectors. Centered on perovskite‐based artificial perception, the graphic illustrates a systematic evolution: starting with fundamental material engineering and device architectures, advancing toward complex functional strategies such as flexible neuromorphic imaging ...
Chenglong Li, Wei Qu, Deepak Kumar, Naini Jain, Nur Wardina Syahirah binti Mohamad Fadil, Nur Najiha binti Ahmad Rasid, Emannuel Kymakis, Maria Vasilopoulou, Chunxiong Bao, Feng Gao, Peng Gao, Sanjeev Kumar Sharma, Mohammad Khaja Nazeeruddin, Abd. Rashid bin Mohd Yusoff, Haotong Wei   +14 more
wiley   +1 more source

Crystal Phase Engineering of Transition‐Metal Dichalcogenides: Pathways to Superior Electrochemical Storage in Lithium–Sulfur Batteries

Carbon Energy, EarlyView.
Crystal phase engineering of TMDs enables enhanced adsorption and catalytic conversion of polysulfides, boosting LSB performance. ABSTRACT Transition‐metal dichalcogenides (TMDs), with their layered structure, high specific surface area, and diverse phase transition properties, offer significant opportunities to tackle the challenges facing lithium ...
Qi Shao, Bo Jiang, Lei Zhang, Xin Wang, Wenxuan Liu, Bin Su, Haihong Wen, Xiaodong Shao, Lutong Shan, Fangyan Liu, Wenwu Li, Wei Ji   +11 more
wiley   +1 more source

Photo‐Switchable FRET‐Enabled Flexible Luminescent Films for Multilevel Optical Security

Carbon Energy, EarlyView.
A light‐gated FRET composite integrates a Tb‐Phen donor and a spiropyran acceptor in a polyurethane matrix. Under 365 nm light, spiropyran is transformed into merocyanine, creating spectral overlap with Tb3+ emission and activating energy transfer. Visible light reverses the switch, restoring green emission and enabling reversible multilevel optical ...
Zihui Liang, Jing Li, Wenhao Zhang, Xiaohong Liao, Huiyi Zong, Lizhi Ren, Congcong Wu, Kai Wang, Jin Qian, Huimin Wu, Hongzhi Hu   +10 more
wiley   +1 more source

Formic‐Acid In Situ Hydrogen Enables Programmable Ru–Pd–Pt/C Trimetallic Interfaces for Durable Acidic HER

Carbon Energy, EarlyView.
Bamboo diaphragm−derived carbon is used as a support to prepare Ru–Pd–Pt/C catalysts through a stepwise reduction strategy. The Ru–Pd interface promotes formic acid activation and induces Pt deposition. The metallic interface of Ru–Pd–Pt/C enables H* generation, transfer, and recombination, thereby improving Pt utilization, acidic HER activity, and PEM
Liangmeng Ni, Aiyue Huang, Xin Feng, Zhijia Liu   +3 more
wiley   +1 more source

Influence of the outer vestibule on permeation and gating in voltage-gated potassium channels

, 2004
Voltage-gated potassium channels are potassium selective ion pores that open in response to membrane depolarization and close in response to hyperpolarization. In addition to their marked preference for potassium over other ions, these channels are noted
Consiglio, Joseph Francis
core   +1 more source

Structure and Dynamics of Porin Loops in Asymmetric Outer Membranes of E. coli

Chemistry – A European Journal, EarlyView.
What are loops of membrane proteins doing within the oligosaccharide coat of cells? This structurally unexplored space is studied by solid‐state NMR, with the outer membrane protein G (OmpG) embedded in asymmetric E. coli outer membrane (OM) vesicles as a paradigmatic example.
Morgane Adélaïde, Jayasubba Reddy Yarava, Florian Lindemann, Massilia Abbas, Nils Cremer, Lisa Gerland, Matthias Hiller, Barth van Rossum, Dirk Linke, Alexander B. Barnes, Edward P. Saliba, Özkan Yildiz, Werner Kühlbrandt, Hartmut Oschkinat   +13 more
wiley   +1 more source