Results 31 to 40 of about 22,345 (254)
Diagnostic guidelines for HLH (HLH-2004 criteria) [15].
, 2021 Diagnostic guidelines for HLH (HLH-2004 criteria) [15].
Lei Wang (6656) +7 more
core +1 more source
Frontiers in Immunology, 2022 BackgroundHemophagocytic lymphohistiocytosis (HLH) is a rapidly fatal disease caused by immune dysregulation. Early initiation of treatment is imperative for saving lives.
Xiao-Jun Xu +15 more
doaj +1 more source
Epidemiological investigation of hemophagocytic lymphohistiocytosis in China
Orphanet Journal of Rare Diseases, 2021 Background Currently, most research on hemophagocytic lymphohistiocytosis (HLH) have focused on etiology and therapy, leaving few epidemiological reports. The published studies of China are mainly regional investigations.
Shuyan Yao +16 more
doaj +1 more source
, 2022 Background: Haemophagocytic lymphohistiocytosis (HLH) is a rare hyper-inflammatory condition with poor outcomes. Objectives: Few population-based estimates of the incidence and survival in adults exist. We aimed to provide these data for England. Methods:
Lucy Elliss‐Brookes +23 more
core +1 more source
Niemann - Pick disease associated with hemophagocytic syndrome
Turkish Journal of Hematology, 2010 Hemophagocytic lymphohistiocytosis (HLH) is a disease characterized by phagocytosis of blood cells by macrophages within the lymphoreticular tissue. It can develop secondary to some diseases or be familial as a result of genetic mutations.
Serap Karaman +3 more
doaj +1 more source
Indian Journal of Medical Specialities, 2022 Hemophagocytic lymphohistiocytosis (HLH) is an inflammatory condition where there is marked cytopenia and large-scale activation of macrophages and CD8+ cytotoxic T cells.
Nitin Rai +4 more
doaj +1 more source
HLH-30/TFEB is abnormally activated in alfa-1(ok3062).
, 2020 (A) Representative images of HLH-30::GFP expression patterns in wild-type or alfa-1(ok3062) C. elegans under well-fed (upper panels) or starvation (lower panels) conditions. Enlarged images of the boxed areas are shown in each panel.
Yon Ju Ji (3359057) +5 more
core +1 more source
Hemophagocytic lymphohistiocytosis secondary to dengue fever
European Journal of Case Reports in Internal MedicineHemophagocytic lymphohistiocytosis (HLH) is a life-threatening hyperinflammatory syndrome often misdiagnosed due to its rarity and overlapping symptoms with sepsis or organ dysfunction.
Simon Kashfi +4 more
doaj +1 more source
HLH-1 Modulates Muscle Proteostasis During Caenorhabditis elegans Larval Development
Frontiers in Cell and Developmental Biology, 2022 Muscle proteostasis is shaped by the myogenic transcription factor MyoD which regulates the expression of chaperones during muscle differentiation. Whether MyoD can also modulate chaperone expression in terminally differentiated muscle cells remains open.
Khairun Nisaa, Anat Ben-Zvi
doaj +1 more source
Data_Sheet_1_High Mortality of HLH in ICU Regardless Etiology or Treatment.docx
, 2021 Background: Adult hemophagocytic lymphohistiocytosis (HLH) is highly lethal in the ICU. The diagnostic and therapeutic emergency that HLH represents is compounded by its unknown pathophysiological mechanisms.
Marc Gainnier (64989) +10 more
core +1 more source