Results 21 to 30 of about 34,282 (300)

CAP2 deficiency delays myofibril actin cytoskeleton differentiation and disturbs skeletal muscle architecture and function [PDF]

open access: bronzeProceedings of the National Academy of Sciences of the United States of America, 2019
Significance Displaced myofibrils termed ring fibers have been reported for human congenital myopathies and for myopathies of unknown etiology, but their natural cause largely remained elusive.
Lara-Jane Kepser   +6 more
openalex   +2 more sources

The oxoglutarate dehydrogenase complex is involved in myofibril growth and Z-disc assembly in Drosophila

open access: yesJournal of Cell Science, 2023
Myofibrils are long intracellular cables specific to muscles, composed mainly of actin and myosin filaments. The actin and myosin filaments are organized into repeated units called sarcomeres, which form the myofibrils.
Nicanor González-Morales   +8 more
semanticscholar   +1 more source

Skeletal Muscle in Cerebral Palsy: From Belly to Myofibril

open access: yesFrontiers in Neurology, 2021
This review will provide a comprehensive, up-to-date review of the current knowledge regarding the pathophysiology of muscle contractures in cerebral palsy.
Jason J. Howard, W. Herzog
semanticscholar   +1 more source

Myofibril and mitochondria morphogenesis are coordinated by a mechanical feedback mechanism in muscle

open access: yesNature Communications, 2020
Complex animals build specialised muscles to match specific biomechanical and energetic needs. Hence, composition and architecture of sarcomeres and mitochondria are muscle type specific.
Jerome Avellaneda   +6 more
semanticscholar   +1 more source

Tension-driven multi-scale self-organisation in human iPSC-derived muscle fibers

open access: yeseLife, 2022
Human muscle is a hierarchically organised tissue with its contractile cells called myofibers packed into large myofiber bundles. Each myofiber contains periodic myofibrils built by hundreds of contractile sarcomeres that generate large mechanical forces.
Qiyan Mao   +16 more
doaj   +1 more source

Lbx2regulates formation of myofibrils [PDF]

open access: yesBMC Developmental Biology, 2009
Skeletal muscle differentiation requires assembly of contractile proteins into organized myofibrils. The Drosophila ladybird homeobox gene (lad) functions in founder cells of the segmental border muscle to promote myoblast fusion and muscle shaping. Tetrapods have two homologous genes (Lbx).
Ochi, Haruki, Westerfield, Monte
openaire   +2 more sources

Right Ventricle Has Normal Myofilament Function But Shows Perturbations in the Expression of Extracellular Matrix Genes in Patients With Tetralogy of Fallot Undergoing Pulmonary Valve Replacement

open access: yesJournal of the American Heart Association: Cardiovascular and Cerebrovascular Disease, 2020
Background Patients with repair of tetralogy of Fallot (rToF) who are approaching adulthood often exhibit pulmonary valve regurgitation, leading to right ventricle (RV) dilatation and dysfunction.
Daniel Brayson   +12 more
doaj   +1 more source

Z-Disk-Associated Plectin (Isoform 1d): Spatial Arrangement, Interaction Partners, and Role in Filamin C Homeostasis

open access: yesCells, 2023
Plectin, a highly versatile cytolinker protein, is crucial for myofiber integrity and function. Accordingly, mutations in the human gene (PLEC) cause several rare diseases, denoted as plectinopathies, with most of them associated with progressive muscle ...
Lilli Winter   +11 more
doaj   +1 more source

Meat myofibril: Chemical composition, sources and its potential for cardiac layers and strong skeleton muscle

open access: yesInternational Journal of Food Properties, 2022
Meat is the richest source of protein and according to meat sources, the protein is composed of different types of amino acids which are completely dependent upon the protein types. Myofibril is basically muscle protein that’s widely present in different
Waseem Khalid   +8 more
doaj   +1 more source

Properties of heat induced blend gel of Peruvian squid (Dosidicus gigas) myofibril protein fortified with millet (Panicum miliaceum L.) flour [PDF]

open access: yesE3S Web of Conferences, 2021
Weak gelation ability and simple nutrient composition of squid myofibril protein limits its further development in surimi production. Millet flour is rich in nutrients and has a good viscoelasticity after heating.
Wang Tian   +4 more
doaj   +1 more source

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